Xie Yao, Qian Yanping, Zou Bingyu
Department of Gynecology and Obstetrics, Sichuan Academy of Medical Sciences & Sichuan Provincial People's Hospital.
Department of Gynecology and Obstetrics, Key Laboratory of Obstetrics & Gynecologic and Pediatric Diseases and Birth Defects of Ministry of Education, West China Second Hospital, Sichuan University, Chengdu, Sichuan, China.
Medicine (Baltimore). 2019 Jan;98(2):e13860. doi: 10.1097/MD.0000000000013860.
Aggressive angiomyxoma (AAM) is a rare and benign invasive mesenchymal stromal tumor predominantly in women at reproductive age. AAM tends to relapse locally and should be differentially diagnosed from other mesenchymal tumors.
We report here a rare case of massive vulvar AAM in a 22-year-old Chinese woman with left labia majora mass with ulcer.
The diagnosis "aggressive angiomyxoma of vulva" was based on clinicopathologic and immunohistochemical features.
A surgery with local excision of the mass was performed.
The patient was discharged 12 days after the surgery. There was no AAM recurrence or metastasis in a period of 12-month follow-up.
The vulvar AAM is a benign and aggressive mesenchymal tumor. In this case, we present the diagnosis, treatment, and prognosis for vulvar AAM. The tumor was removed completely by the surgery, but a long-term follow-up is requisite for surveilling on recurrence.
侵袭性血管黏液瘤（AAM）是一种罕见的良性侵袭性间充质基质肿瘤，主要发生于育龄期女性。AAM容易局部复发，需要与其他间充质肿瘤进行鉴别诊断。
我们在此报告一例罕见的巨大外阴AAM病例，患者为一名22岁中国女性，左侧大阴唇有肿物伴溃疡。
“外阴侵袭性血管黏液瘤”的诊断基于临床病理和免疫组化特征。
进行了肿物局部切除手术。
患者术后12天出院。在12个月的随访期内，未出现AAM复发或转移。
外阴AAM是一种良性但具有侵袭性的间充质肿瘤。在本病例中，我们展示了外阴AAM的诊断、治疗和预后。肿瘤通过手术完全切除，但需要长期随访以监测复发情况。
