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与肠息肉病相关的纤维毛囊瘤、毛发盘状瘤和皮赘(Birt-Hogg-Dubé综合征)

Fibrofolliculomas, tricodiscomas and acrochordons (Birt-Hogg-Dubé) associated with intestinal polyposis.

作者信息

Rongioletti F, Hazini R, Gianotti G, Rebora A

出版信息

Clin Exp Dermatol. 1989 Jan;14(1):72-4. doi: 10.1111/j.1365-2230.1989.tb00890.x.

DOI:10.1111/j.1365-2230.1989.tb00890.x
PMID:2805394
Abstract

We describe a patient with multiple fibrofolliculomas (FF), tricodiscomas (TD) and acrochordons (Birt-Hogg-Dubé) associated with intestinal polyps. One of the polyps presented histological features of marked dysplasia. This association may not be fortuitous and suggests that patients with multiple hamartomas of the perifollicular connective tissue should be examined periodically for intestinal polyps before malignancy develops.

摘要

我们描述了一名患有多发性纤维毛囊瘤(FF)、毛发上皮瘤(TD)和皮赘(Birt-Hogg-Dubé综合征)并伴有肠息肉的患者。其中一个息肉呈现出明显发育异常的组织学特征。这种关联可能并非偶然,提示毛囊周围结缔组织多发错构瘤患者在发生恶性病变之前应定期检查是否存在肠息肉。

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Fibrofolliculomas, tricodiscomas and acrochordons (Birt-Hogg-Dubé) associated with intestinal polyposis.与肠息肉病相关的纤维毛囊瘤、毛发盘状瘤和皮赘(Birt-Hogg-Dubé综合征)
Clin Exp Dermatol. 1989 Jan;14(1):72-4. doi: 10.1111/j.1365-2230.1989.tb00890.x.
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