Chauhan Richa S, Singh Dheeraj K, Guha Bishwarup, Kumar Ishan, Verma Ashish
Department of Radiodiagnosis and Imaging, Institute of Medical sciences, Banaras Hindu University, Varanasi, Uttar Pradesh, India.
Department of Urology, Institute of Medical sciences, Banaras Hindu University, Varanasi, Uttar Pradesh, India.
Indian J Radiol Imaging. 2017 Apr-Jun;27(2):148-151. doi: 10.4103/ijri.IJRI_444_16.
Rhabdomyosarcoma (RMS) is a malignant mesenchymal tumor arising from the embryonal muscle cells (rhabdomyoblasts), and is the most common soft tissue sarcoma in children and young adults accounting for 4-6% of all malignancies in this age group. Though rare overall, embryonal rhabdomyosarcoma is the most common malignancy arising in the pediatric female genitourinary tract with sarcoma botryoides being the most common variant of the tumor. In young and adolescent individuals, the cervix and uterus are affected; whereas in infants, vaginal lesions are more common. Imaging plays a crucial role not only in the initial diagnosis but also in long-term follow-up of genital RMS. We describe a rare case of embryonal rhabdomyosarcoma of the vagina occurring in a 23-year-old female who presented with abnormal vaginal bleeding ever since she was a child.
横纹肌肉瘤（RMS）是一种起源于胚胎肌肉细胞（成横纹肌细胞）的恶性间叶组织肿瘤，是儿童和年轻成人中最常见的软组织肉瘤，占该年龄组所有恶性肿瘤的4%-6%。虽然总体上较为罕见，但胚胎性横纹肌肉瘤是小儿女性泌尿生殖道最常见的恶性肿瘤，葡萄状肉瘤是该肿瘤最常见的变异型。在青少年个体中，宫颈和子宫会受到影响；而在婴儿中，阴道病变更为常见。影像学不仅在生殖器RMS的初始诊断中起着关键作用，而且在其长期随访中也至关重要。我们描述了一例罕见的阴道胚胎性横纹肌肉瘤病例，患者为一名23岁女性，自幼就出现阴道异常出血。
