Hope Charity B, Pincus Laura B
Department of Pathology, UCSF Dermatopathology Section, University of California, San Francisco, 1701 Divisidero Street, Room 280, San Francisco, CA 94115, USA.
Department of Pathology, UCSF Dermatopathology Section, University of California, San Francisco, 1701 Divisidero Street, Room 280, San Francisco, CA 94115, USA; Department of Dermatology, UCSF Dermatopathology Section, University of California, San Francisco, 1701 Divisidero Street, Room 280, San Francisco, CA 94115, USA.
Clin Lab Med. 2017 Sep;37(3):547-574. doi: 10.1016/j.cll.2017.05.009.
B-cell lymphomas represent approximately 20% to 25% of primary cutaneous lymphomas. Within this group, most cases (>99%) are encompassed by 3 diagnostic entities: primary cutaneous marginal zone lymphoma, primary cutaneous follicle center lymphoma, and primary cutaneous diffuse large B-cell lymphoma, leg type. In this article, the authors present clinical, histopathologic, immunophenotypic, and molecular features of each of these entities and briefly discuss the rarer intravascular large B-cell lymphoma.
B细胞淋巴瘤约占原发性皮肤淋巴瘤的20%至25%。在这一类别中,大多数病例(>99%)包含在3种诊断实体中:原发性皮肤边缘区淋巴瘤、原发性皮肤滤泡中心淋巴瘤和原发性皮肤弥漫性大B细胞淋巴瘤,腿部型。在本文中,作者介绍了这些实体各自的临床、组织病理学、免疫表型和分子特征,并简要讨论了较为罕见的血管内大B细胞淋巴瘤。