Campbell A M, Finley G A
Department of Anaesthesia, Izaak Walton Killam Children's Hospital, Dalhousie University, Halifax, Nova Scotia.
Can J Anaesth. 1989 Jan;36(1):89-93. doi: 10.1007/BF03010895.
Friedreich's ataxia is an inherited neuromuscular disorder often associated with significant cardiac disease. We report a case of Friedreich's ataxia in a 13-year-old girl with ulcerative colitis and hypertrophic cardiomyopathy who was successfully managed for subtotal colectomy with general anaesthesia and epidural narcotic. Anaesthetic considerations included the maintenance of fluid volume and stable cardiovascular variables in the intra- and postoperative periods.
弗里德赖希共济失调是一种遗传性神经肌肉疾病，常伴有严重的心脏疾病。我们报告一例13岁患溃疡性结肠炎和肥厚型心肌病的弗里德赖希共济失调女孩，她接受了全身麻醉和硬膜外麻醉下的次全结肠切除术，并成功完成手术。麻醉方面的考虑包括在术中和术后维持血容量和稳定心血管参数。
