Aksoy Emine, Aktaş Oğuz, Tokgöz Fatma, Kongar Nilufer, Gökşenoğlu Nezihe, Bodur Yasemin, Güran Salih, Sevim Tülin
Clinic of Chest Diseases, Süreyyapaşa Chest Diseases Hospital, İstanbul, Turkey.
Department of Radiology, Sonomed Imaging Centre, İstanbul, Turkey.
Turk Thorac J. 2015 Jan;16(1):36-42. doi: 10.5152/ttd.2014.4052. Epub 2014 Jul 11.
Swyer-James-MacLeod syndrome or unilateral hyperlucent lung syndrome is a rare disease characterised by hypoplasia of the pulmonary artery, unilateral hyperlucent lung and usually bronchiectasis. The syndrome was first described by Swyer and James in 1953 in a child case, and in the following year 9 adult cases were reported by MacLeod. We retrospectively reviewed 6 adult cases, five female and one male, who were followed-up with the diagnosis of Swyer-James-MacLeod syndrome between 2005 and 2012 in our clinic. The clinical and radiological features of these 6 cases are presented in the light of the literature.
斯怀尔-詹姆斯-麦克劳德综合征或单侧肺透亮综合征是一种罕见疾病,其特征为肺动脉发育不全、单侧肺透亮,且通常伴有支气管扩张。该综合征于1953年由斯怀尔和詹姆斯首次在一例儿童病例中描述,次年麦克劳德报告了9例成人病例。我们回顾性分析了2005年至2012年期间在我院确诊为斯怀尔-詹姆斯-麦克劳德综合征并接受随访的6例成人病例,其中5例女性,1例男性。结合文献对这6例病例的临床和放射学特征进行了阐述。