Gebreselassie Agazi, Bukhari Majidah, Awan Ahmad, Khashab Mouen
Gastroenterology, Howard University Hospital.
John Hopkins University Hospital.
Cureus. 2018 Jan 9;10(1):e2046. doi: 10.7759/cureus.2046.
Portal vein thrombosis with cavernous transformation is a rare cause of biliary obstruction. Portal biliopathy is a term that refers to abnormalities in the intrahepatic and extrahepatic biliary tract, gall bladder, and cystic duct secondary to portal hypertension. Patients may be asymptomatic, but they can also present with abdominal pain, jaundice, and fever. We present the case of a 61-year-old Caucasian female who presented with generalized weakness, dark urine, and yellow skin for three days' duration. Magnetic resonance cholangiopancreatography (MRCP) showed extrahepatic and intrahepatic biliary ductal dilatation. Endoscopic retrograde cholangiopancreatography (ERCP) with cholangioscopy was used to make the diagnosis of portal biliopathy. This case highlights the importance of ERCP with cholangioscopy in the diagnosis and management of recurrent portal biliopathy.
门静脉海绵样变性伴血栓形成是导致胆道梗阻的罕见原因。门静脉性肝病是一个术语,指继发于门静脉高压的肝内和肝外胆道、胆囊及胆囊管的异常。患者可能无症状,但也可能出现腹痛、黄疸和发热。我们报告一例61岁白种女性病例,她出现全身乏力、尿色加深和皮肤发黄3天。磁共振胆胰管造影(MRCP)显示肝外和肝内胆管扩张。采用内镜逆行胰胆管造影(ERCP)及胆管镜检查确诊为门静脉性肝病。该病例强调了ERCP及胆管镜检查在复发性门静脉性肝病诊断和治疗中的重要性。