Glibbery Natalia, Muscat Kenneth, Cascarini Luke
Department of Head and Neck Surgery, Guy's and St Thomas' NHS Foundation Trust, London SE1 9RT, UK.
J Surg Case Rep. 2018 Apr 9;2018(4):rjy067. doi: 10.1093/jscr/rjy067. eCollection 2018 Apr.
Kimura's disease is a rare disease of unknown aetiology, commonly presenting with slow-growing head and neck subcutaneous nodules, lymphadenopathy, eosinophilia and elevated immunoglobulin E. This report describes a very rare case of a 41-year-old female, of White-British ethnicity, with a new diagnosis of Kimura's disease of the parotid gland and associated cutaneous features. The patient was investigated for 3 years before a diagnosis of Kimura's disease was reached. A superficial parotidectomy was undertaken and no recurrence was observed in the 20 months following surgery. Kimura's disease is easily misdiagnosed, owing to lack of clinical awareness. This case report highlights the troubling symptomatology as well as complexities of diagnosis and management of Kimura's disease. A high level of clinical suspicion is required, for patients of any ethnicity and sex presenting with features consistent with the disease, in order for prompt diagnosis, investigation and management to be achieved.
木村病是一种病因不明的罕见疾病,通常表现为生长缓慢的头颈部皮下结节、淋巴结病、嗜酸性粒细胞增多和免疫球蛋白E升高。本报告描述了一例非常罕见的病例,患者为41岁的英国白人女性,新诊断为腮腺木村病并伴有相关皮肤表现。该患者在确诊木村病之前接受了3年的检查。进行了腮腺浅叶切除术,术后20个月未观察到复发。由于缺乏临床认识,木村病很容易被误诊。本病例报告强调了木村病令人困扰的症状以及诊断和管理的复杂性。对于任何种族和性别的患者,只要出现与该病相符的特征,都需要高度的临床怀疑,以便能够及时进行诊断、检查和管理。