You Di, Wang Qilin, Jiang Wei, Lin Lin, Yi Tianjin, Zhao Lingjun, Li Maomao, Wang Ping
Department of Obstetrics and Gynecology, West China Second University Hospital, Sichuan University.
Key Laboratory of Birth Defects and Related Diseases of Women and Children (Sichuan University), Ministry of Education.
Medicine (Baltimore). 2018 Apr;97(17):e0536. doi: 10.1097/MD.0000000000010536.
Primary leiomyosarcoma (LMS) of the fallopian tube is extremely uncommon. To the best of our knowledge, so far only 21 cases of primary fallopian tube LMS have been reported in English-language literature. No new case has been reported in the past 7 years.
A 44-year-old premenopausal patient presented with a 5-day history of lower abdominal pain.
Pelvic ultrasonography detected an 8.8 × 7.8 × 6.5 cm solid and cystic mass in the left side of the pelvic cavity. The tumor was diagnosed as a primary fallopian tube LMS on paraffin section.
The patient treated surgically followed by 4 cycles of postoperative chemotherapy with dacarbazine and DDP.
The patient succumbed to the disease 27 months after the initial therapy.
Tube LMS is a rare malignant tumor with unknown etiology, difficult early diagnosis, highly invasiveness, high local recurrence and distant metastasis rate, rapid progress, and poor prognosis. It is extremely rare so we can only summarize limited experience from limited data. Every case of tubal LMS is worth being reported.
原发性输卵管平滑肌肉瘤(LMS)极为罕见。据我们所知,迄今为止英文文献中仅报道了21例原发性输卵管LMS。在过去7年中未报告新病例。
一名44岁的绝经前患者,有5天的下腹痛病史。
盆腔超声检查在盆腔左侧发现一个8.8×7.8×6.5 cm的实性和囊性肿块。肿瘤经石蜡切片诊断为原发性输卵管LMS。
患者接受了手术治疗,术后用达卡巴嗪和顺铂进行了4个周期的化疗。
患者在初始治疗后27个月死于该疾病。
输卵管LMS是一种病因不明的罕见恶性肿瘤,早期诊断困难,侵袭性强,局部复发和远处转移率高,进展迅速,预后差。它极为罕见,因此我们只能从有限的数据中总结有限的经验。每一例输卵管LMS病例都值得报告。