Elsheshtawy Moustafa O, Mahmoud Ahmed N, Abdelghany Mahmoud, Suen Ida H, Sadiq Adnan, Shani Jacob
Division of Cardiovascular Medicine, Department of Medicine, Maimonides Medical Center, Brooklyn, NY, USA.
Division of Cardiovascular Medicine, Department of Medicine, Coney Island Hospital, Brooklyn, NY, USA.
Pacing Clin Electrophysiol. 2018 Jul;41(7):854-865. doi: 10.1111/pace.13380. Epub 2018 Jun 20.
Hypertrophic cardiomyopathy (HCM) with or without left ventricular apical aneurysm (LVA) had been studied in the past. Midventricular obstruction associated with HCM and LVA is a unique entity that has not been distinguished previously as a separate phenotypic disease in HCM patients.
A systematic review of Pubmed and Google Scholar was conducted from inception until September 2017 for all observational studies conducted on HCM with midventricular obstruction and LVA.
A total of 94 patients from 39 studies were included in our analysis. The mean age of the patients was 58.05 ± 11.76 years with 59.6% being males. The most common electrocardiographic finding was T wave inversion occurring in 13.8% of the cases followed by ST elevation (9.5%). Maximal left ventricle (LV) wall thickness was reported 18.89 ± 5.19 mm on transthoracic echocardiography and paradoxical jet flow was detected in 29.8% of patients. Beta-blockers (58.5%) were the most common drug therapy at baseline and amiodarone (10.6%) was the most common antiarrhythmic used for ventricular tachycardia (VT). The most common complication, VT, occurred in 39.3% of cases and the incidence of all-cause mortality was 13.8 % over 16 ± 20.1 months follow-up. Implantable cardioverter defibrillator (ICD) was used in 37.2% of patients; 25.7% of patients with ICD received appropriate shock therapy.
HCM with LVA and midventricular obstruction is a unique entity that appears to be associated with high incidence of morbidity and mortality. Thus, early diagnosis and therapeutic intervention is recommended for management of this condition.
肥厚型心肌病(HCM)伴或不伴左心室心尖部室壁瘤(LVA)在过去已有研究。与HCM和LVA相关的心室中部梗阻是一种独特的情况,以前在HCM患者中未被作为一种单独的表型疾病区分出来。
对PubMed和谷歌学术进行系统检索,涵盖从开始到2017年9月所有关于伴有心室中部梗阻和LVA的HCM的观察性研究。
我们的分析纳入了39项研究中的94例患者。患者的平均年龄为58.05±11.76岁,男性占59.6%。最常见的心电图表现是T波倒置,发生率为13.8%,其次是ST段抬高(9.5%)。经胸超声心动图报告的最大左心室(LV)壁厚度为18.89±5.19mm,29.8%的患者检测到矛盾性射流。β受体阻滞剂(58.5%)是基线时最常用的药物治疗,胺碘酮(10.6%)是用于室性心动过速(VT)最常用的抗心律失常药物。最常见的并发症是VT,发生率为