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混合性结缔组织病患者的淋巴细胞间质性肺炎——一例报告

Lymphocytic interstitial pneumonia in a patient with mixed connective tissue disease - A case report.

作者信息

Kuo Chin-Wei, Chang Kung-Chao, Chang Han-Yu, Huang Tang-Hsiu

机构信息

Division of Chest Medicine, Department of Internal Medicine, National Cheng Kung University Hospital, College of Medicine, National Cheng Kung University, Tainan, Taiwan.

Department of Pathology, National Cheng Kung University Hospital, College of Medicine, National Cheng Kung University, Tainan, Taiwan.

出版信息

Respir Med Case Rep. 2018 Jun 5;25:12-17. doi: 10.1016/j.rmcr.2018.06.003. eCollection 2018.

Abstract

Lymphocytic interstitial pneumonia (LIP) is an uncommon interstitial lung disease that is characterized by an interstitial infiltrate of lymphoplasmacytic cells. While idiopathic LIP appears to be extremely rare, most reported cases of LIP have been associated with coexisting immune derangements, particularly autoimmune diseases such as Sjögren's syndrome. In this report, we describe the presentation of LIP in a patient with underlying mixed connective tissue disease.

摘要

淋巴细胞间质性肺炎(LIP)是一种罕见的间质性肺疾病,其特征为淋巴细胞和浆细胞的间质浸润。虽然特发性LIP似乎极为罕见,但大多数报道的LIP病例都与并存的免疫紊乱有关,尤其是自身免疫性疾病,如干燥综合征。在本报告中,我们描述了一名患有潜在混合性结缔组织病患者的LIP表现。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3460/5991914/ac742988e72b/gr1.jpg

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