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Intestinal Involvement in Systemic Sclerosis: A Clinical Review.系统性硬化症的肠道累及:临床综述。
Dig Dis Sci. 2018 Apr;63(4):834-844. doi: 10.1007/s10620-018-4977-8. Epub 2018 Feb 21.
2
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Ann Med Surg (Lond). 2017 Sep 30;23:25-27. doi: 10.1016/j.amsu.2017.09.010. eCollection 2017 Nov.
3
Successful treatment of pneumatosis intestinalis with associated pneumoperitoneum and ileus with hyperbaric oxygen therapy.高压氧疗法成功治疗伴有气腹和肠梗阻的肠壁囊样积气症。
BMJ Case Rep. 2017 May 30;2017:bcr-2017-219209. doi: 10.1136/bcr-2017-219209.
4
Current management of the gastrointestinal complications of systemic sclerosis.系统性硬化症的胃肠道并发症的当前管理。
Nat Rev Gastroenterol Hepatol. 2016 Aug;13(8):461-72. doi: 10.1038/nrgastro.2016.99. Epub 2016 Jul 6.
5
An approach to pneumatosis intestinalis: Factors affecting your management.小肠积气的处理方法:影响治疗的因素
Int J Surg Case Rep. 2015;6C:133-7. doi: 10.1016/j.ijscr.2014.12.007. Epub 2014 Dec 12.
6
Pneumatosis intestinalis with a focus on hyperbaric oxygen therapy.肠积气,重点介绍高压氧疗法。
Mayo Clin Proc. 2014 May;89(5):697-703. doi: 10.1016/j.mayocp.2014.01.026.
7
Pneumatosis cystoides intestinalis: a rare benign cause of pneumoperitoneum.肠壁囊样积气症:气腹的一种罕见良性病因。
Case Rep Radiol. 2013;2013:353245. doi: 10.1155/2013/353245. Epub 2013 Aug 1.
8
A systematic analysis of pneumatosis cystoids intestinalis.肠气囊肿症的系统分析。
World J Gastroenterol. 2013 Aug 14;19(30):4973-8. doi: 10.3748/wjg.v19.i30.4973.
9
Pneumatosis cystoides intestinalis in scleroderma-related conditions.硬皮病相关疾病的肠囊样积气。
Intern Med J. 2012 Mar;42(3):323-9. doi: 10.1111/j.1445-5994.2011.02557.x.
10
Gastrointestinal manifestations of systemic sclerosis.系统性硬化症的胃肠道表现
Dig Dis Sci. 2008 May;53(5):1163-74. doi: 10.1007/s10620-007-0018-8. Epub 2007 Oct 13.

系统性硬化症相关肠壁囊样积气的联合治疗

Combination therapy for systemic sclerosis-associated pneumatosis intestinalis.

作者信息

Koysombat Kanyada, Capanna Maria Vittoria, Stafford Nina, Orchard Tim

机构信息

Department of Gastroenterology, Imperial College Healthcare NHS Trust, London, UK.

出版信息

BMJ Case Rep. 2018 Jul 11;2018:bcr-2018-225068. doi: 10.1136/bcr-2018-225068.

DOI:10.1136/bcr-2018-225068
PMID:30002210
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6047708/
Abstract

We present a case of a patient with pneumatosis intestinalis and pneumoperitoneum secondary to gastrointestinal systemic sclerosis, who presented following recurrent accident and emergency attendances with abdominal pain. Pneumatosis intestinalis is a rare complication of systemic sclerosis; management approaches focus largely on exclusion of life-threatening surgical pathologies and subsequent symptom control. To date, there are still no established gold-standard treatment strategy and no large-scale trial data to support a specific management strategy. We describe a case of successful medical management with a combination of antimicrobial, elemental diet and high-flow inhalation oxygen therapy, with supporting evidence of CT image confirming resolution. This case therefore contributes to the literature, being the first to report both symptomatic and radiological improvement following combination therapy without the need for surgical intervention.

摘要

我们报告一例因胃肠道系统性硬化症继发肠壁积气和腹腔积气的患者,该患者因反复出现腹痛而多次到急诊就诊。肠壁积气是系统性硬化症的一种罕见并发症;管理方法主要集中在排除危及生命的外科病变以及随后的症状控制上。迄今为止,仍没有既定的金标准治疗策略,也没有大规模试验数据支持特定的管理策略。我们描述了一例通过抗菌药物、要素饮食和高流量吸氧疗法联合成功进行药物治疗的病例,CT图像的支持证据证实了病情缓解。因此,该病例为文献提供了资料,是首例报道联合治疗后症状和影像学均有改善且无需手术干预的病例。