Low serum haptoglobin and blood films suggest intravascular hemolysis contributes to severe anemia in hereditary hemorrhagic telangiectasia.
作者信息
Thielemans Lieze, Layton D Mark, Shovlin Claire L
机构信息
Imperial College School of Medicine, Imperial College London.
Haematology, Imperial College London.
出版信息
Haematologica. 2019 Apr;104(4):e127-e130. doi: 10.3324/haematol.2018.205682. Epub 2018 Oct 18.
Abstract
摘要
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Low serum haptoglobin and blood films suggest intravascular hemolysis contributes to severe anemia in hereditary hemorrhagic telangiectasia.低血清结合珠蛋白和血涂片提示血管内溶血导致遗传性出血性毛细血管扩张症中的严重贫血。
Haematologica. 2019 Apr;104(4):e127-e130. doi: 10.3324/haematol.2018.205682. Epub 2018 Oct 18.
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European Reference Network For Rare Vascular Diseases (VASCERN) Outcome Measures For Hereditary Haemorrhagic Telangiectasia (HHT).欧洲罕见血管疾病参考网络（VASCERN）遗传性出血性毛细血管扩张症（HHT）结局指标。
Orphanet J Rare Dis. 2018 Aug 15;13(1):136. doi: 10.1186/s13023-018-0850-2.
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Cerebral Abscess Associated With Odontogenic Bacteremias, Hypoxemia, and Iron Loading in Immunocompetent Patients With Right-to-Left Shunting Through Pulmonary Arteriovenous Malformations.免疫功能正常患者右向左分流通过肺动静脉畸形并发牙源性菌血症、低氧血症和铁过载相关脑脓肿。
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