Lucas R V, Lock J E, Tandon R, Edwards J E
Department of Pediatrics, Variety Club Heart Hospital, University of Minnesota, Minneapolis.
Am J Cardiol. 1988 Aug 1;62(4):292-300. doi: 10.1016/0002-9149(88)90227-5.
Among 49 heart specimens with total anomalous pulmonary venous connection (TAPVC), obstruction to pulmonary venous flow was present in all 13 cases with TAPVC below the diaphragm and in 53% of 36 cases with TAPVC above the diaphragm. Obstruction was produced by extrinsic pressures on the vein, intrinsic narrowing of the vein, or both. The histology of the narrowed veins was extremely variable, ranging from atrophy of the vein wall to hypertrophy of intima, media-adventitia, or both. Balloon dilation of narrowed veins was performed in 3 cases, without clinical or anatomic evidence of success.
在49例完全性肺静脉异位连接(TAPVC)心脏标本中,13例膈肌以下TAPVC患者均存在肺静脉血流梗阻,36例膈肌以上TAPVC患者中有53%存在梗阻。梗阻是由静脉外部压力、静脉内部狭窄或两者共同作用引起的。狭窄静脉的组织学表现差异极大,从静脉壁萎缩到内膜、中膜-外膜肥大不等。对3例狭窄静脉进行了球囊扩张,但无临床或解剖学成功证据。