Paluszkiewicz Jerzy, Krasinska Beata, Milting Hendrik, Gummert Jan, Pyda Małgorzata
Cardiology Institute and Clinic, Poznan University of Medical Sciences, Poznan, Poland.
Hypertensiology, Angiology and Internal Medicine Institute, Poznan University of Medical Sciences, Poznan, Poland.
Kardiochir Torakochirurgia Pol. 2018 Dec;15(4):246-253. doi: 10.5114/kitp.2018.80922. Epub 2018 Dec 31.
Apical hypertrophic cardiomyopathy (AHCM) is a rare form of hypertrophic cardiomyopathy, occasionally resulting in severe complications. The paper covers the etiology and pathogenesis of AHCM, different imaging methods and characteristic appearance of the disease in each of them. Echocardiography and cardiovascular magnetic resonance imaging (CMR) are known to be the most valuable imaging methods. Moreover, this review presents medical and surgical treatment, as well as the clinical course and prognosis. Despite possible morbid events the overall cardiovascular mortality rate of AHCM patients is low, and the prognosis is relatively optimistic.
心尖肥厚型心肌病(AHCM)是肥厚型心肌病的一种罕见形式,偶尔会导致严重并发症。本文涵盖了AHCM的病因和发病机制、不同的成像方法以及每种方法中该疾病的特征表现。超声心动图和心血管磁共振成像(CMR)是已知最有价值的成像方法。此外,本综述还介绍了内科和外科治疗,以及临床病程和预后。尽管可能发生不良事件,但AHCM患者的总体心血管死亡率较低,预后相对乐观。