Al-Harthi Adil H, Khan Patan M, Al Marwani Marwan
Department of Medicine, King Fahd Armed Forces Hospital, Jeddah, Saudi Arabia.
Department of Radiology, King Fahd Armed Forces Hospital, Jeddah, Saudi Arabia.
Saudi J Med Med Sci. 2016 Sep-Dec;4(3):222-224. doi: 10.4103/1658-631X.188259. Epub 2016 Aug 11.
Multiple liver cysts can be an isolated disease (isolated polycystic liver disease [PLD]) or they can be part of multi-organ involvement in other diseases, such as adult autosomal dominant polycystic disease (APD), which is the most frequently inherited polycystic disease affecting 1 in 1,000 of the population. About 33% of APD patients are expected to develop PLD. Cysts in the liver, as opposed to cysts in the kidney, grow dramatically in number and size. They are usually asymptomatic but may present with signs and symptoms of compression of adjacent organs as the cysts grow. We present a case of a 73 year-old female patient with PLD and a large (25 × 19 × 18 cm) infected cyst which caused the displacement of the inferior vena cava, right kidney, and pancreas. We also discuss the management of this patient along with a review of the literature.
多发性肝囊肿可以是一种孤立性疾病（孤立性多囊肝病[PLD]），也可以是其他疾病多器官受累的一部分，如成人常染色体显性多囊病（APD），这是最常见的遗传性多囊病，影响着千分之一的人群。预计约33%的APD患者会发展为PLD。与肾囊肿不同，肝囊肿的数量和大小会急剧增加。它们通常无症状，但随着囊肿的生长，可能会出现压迫相邻器官的体征和症状。我们报告一例73岁女性PLD患者，其有一个巨大（25×19×18 cm）的感染性囊肿，导致下腔静脉、右肾和胰腺移位。我们还将讨论该患者的治疗，并对相关文献进行综述。
