Kumar N Girish, Maurya Brig S, Sudeep Col S
1Department of Oral and Maxillofacial Surgery, PMS College of Dental Science and Research, Golden Hills, Vattapara, Thiruvananthapuram, 695028 India.
Command Hospital, Chandimandir, India.
J Maxillofac Oral Surg. 2019 Jun;18(2):210-216. doi: 10.1007/s12663-018-1147-7. Epub 2018 Aug 18.
Parry Romberg Syndrome or Progressive Hemifacial Atrophy is a rare disease usually affecting one side of face with loss of soft and hard tissues. The disease appears suddenly and is usually self-limiting in 2-10 years time. The loss of soft and hard tissue leads to aesthetic and functional deficits which are compounded by the presence of associated symptoms like neuralgia, migraine, epilepsy and ocular involvement. The degree of deformity depends on the age at which the disease manifests first; the younger the age, the more severe the deformity. These patients undergo severe psychological trauma and social problems. The exact etiology is not known, and treatment is largely cosmetic. A report of three cases and a literature review is presented.
帕里-罗姆伯格综合征或进行性半侧颜面萎缩是一种罕见疾病，通常影响面部一侧，导致软硬组织丧失。该病起病突然，通常在2至10年内自行缓解。软硬组织的丧失会导致美学和功能缺陷，而神经痛、偏头痛、癫痫和眼部受累等相关症状会使这些缺陷更加复杂。畸形程度取决于疾病首次出现时的年龄；年龄越小，畸形越严重。这些患者会遭受严重的心理创伤和社会问题。确切病因尚不清楚，治疗主要是美容方面的。本文报告了三例病例并进行了文献综述。
