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伴有QT间期延长的应激性心肌病:一种非典型表现。

"Takotsubo cardiomyopathy presenting with QT prolongation: an atypical presentation.".

作者信息

Ali Zain, Zain Muhammad Abdullah, Khan Mariya, Ahmad Asrar, Abbas Hassan, Ashfaq Ammar Ali

机构信息

Resident Physician, Internal medicine, Abington Memorial Hospital, Abington, PA, USA.

Department of Internal Medicine, Sheikh Zayed Medical College and Hospital, Rahim Yar Khan, Pakistan.

出版信息

J Community Hosp Intern Med Perspect. 2019 Apr 12;9(2):171-174. doi: 10.1080/20009666.2019.1598229. eCollection 2019 Apr.

DOI:10.1080/20009666.2019.1598229
PMID:31044052
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6484497/
Abstract

Takotasubo Cardiomyopathy (TCM), also known as broken heart syndrome, is a syndrome of transient and reversible cardiac dysfunction in the absence of obstructive coronary artery disease following an unpleasant emotional event. TCM commonly presents as chest pain mimicking acute coronary syndrome (ACS) in character. The most common electrocardiogram (EKG) findings associated with TCM are ST-segment elevation or T wave inversion. Herein, we present a case of TCM in an individual who presented with a sudden onset chest pressure following a stressful event. She was found to have QT interval prolongation on EKG and elevated troponins. Initially thought to have non-ST elevation myocardial infarction (NSTEMI). Cardiac catheterization did not reveal coronary artery disease. The ventriculography suggested apical ballooning and the diagnosis of TCM with atypical EKG presentation. Our case is unique as we describe an atypical electrocardiographic presentation of TCM. Our case emphasizes that physicians should refrain from prescribing QT-prolonging drugs to patients with TCM, to avert potential QT prolongation and progression to torsade de pointes (TDP).

摘要

应激性心肌病(TCM),也被称为心碎综合征,是一种在不愉快情绪事件后出现的、无阻塞性冠状动脉疾病情况下的短暂且可逆的心脏功能障碍综合征。TCM通常表现为类似急性冠状动脉综合征(ACS)特征的胸痛。与TCM相关的最常见心电图(EKG)表现是ST段抬高或T波倒置。在此,我们报告一例应激性心肌病病例,该患者在压力事件后突然出现胸部压迫感。她的心电图显示QT间期延长,肌钙蛋白升高。最初被认为患有非ST段抬高型心肌梗死(NSTEMI)。心脏导管检查未发现冠状动脉疾病。心室造影显示心尖部气球样改变,诊断为具有非典型心电图表现的应激性心肌病。我们的病例很独特,因为我们描述了应激性心肌病的非典型心电图表现。我们的病例强调医生不应给应激性心肌病患者开可延长QT间期的药物,以避免潜在的QT间期延长和发展为尖端扭转型室性心动过速(TDP)。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c1c6/6484497/f439ad4e349a/ZJCH_A_1598229_F0004_OC.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c1c6/6484497/59225011888b/ZJCH_A_1598229_F0001_OC.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c1c6/6484497/0641c6ec734b/ZJCH_A_1598229_F0002_OC.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c1c6/6484497/d45d852e8efe/ZJCH_A_1598229_F0003_B.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c1c6/6484497/f439ad4e349a/ZJCH_A_1598229_F0004_OC.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c1c6/6484497/59225011888b/ZJCH_A_1598229_F0001_OC.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c1c6/6484497/0641c6ec734b/ZJCH_A_1598229_F0002_OC.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c1c6/6484497/d45d852e8efe/ZJCH_A_1598229_F0003_B.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c1c6/6484497/f439ad4e349a/ZJCH_A_1598229_F0004_OC.jpg

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本文引用的文献

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QT Prolongation and Clinical Outcomes in Patients with Takotsubo Cardiomyopathy.应激性心肌病患者的QT间期延长与临床结局
Pacing Clin Electrophysiol. 2016 Jun;39(6):607-11. doi: 10.1111/pace.12864. Epub 2016 May 4.
2
Takotsubo cardiomyopathy, a new concept of cardiomyopathy: clinical features and pathophysiology.应激性心肌病,一种心肌病的新概念:临床特征与病理生理学
Int J Cardiol. 2015 Mar 1;182:297-303. doi: 10.1016/j.ijcard.2014.12.116. Epub 2014 Dec 30.
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Takotsubo cardiomyopathy a short review.应激性心肌病:简要综述
Curr Cardiol Rev. 2013 Aug;9(3):191-6. doi: 10.2174/1573403x11309030003.
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Electrocardiographic changes in Takotsubo cardiomyopathy.应激性心肌病的心电图变化
Pacing Clin Electrophysiol. 2011 Oct;34(10):1278-82. doi: 10.1111/j.1540-8159.2011.03151.x. Epub 2011 Jun 14.
5
Takotsubo cardiomyopathy: assessment with cardiac MRI.心肌应变:心脏 MRI 的评估。
AJR Am J Roentgenol. 2010 Aug;195(2):W139-45. doi: 10.2214/AJR.09.3369.
6
Upregulation of heme oxygenase-1 in an animal model of Takotsubo cardiomyopathy.应激性心肌病动物模型中血红素加氧酶-1的上调
Circ J. 2009 Jun;73(6):1141-6. doi: 10.1253/circj.cj-08-0988. Epub 2009 Apr 16.
7
Takotsubo cardiomyopathy and QT interval prolongation: who are the patients at risk for torsades de pointes?应激性心肌病与QT间期延长:哪些患者有发生尖端扭转型室速的风险?
J Electrocardiol. 2009 Jul-Aug;42(4):353-357.e1. doi: 10.1016/j.jelectrocard.2009.01.005. Epub 2009 Mar 3.
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Left ventricular apical ballooning syndrome: prevalence, clinical characteristics and pathogenetic mechanisms in a European population.左心室尖部气球样变综合征:欧洲人群中的患病率、临床特征及发病机制
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Stress (Takotsubo) cardiomyopathy--a novel pathophysiological hypothesis to explain catecholamine-induced acute myocardial stunning.应激(应激性心肌病)——一种解释儿茶酚胺诱导的急性心肌顿抑的新病理生理假说。
Nat Clin Pract Cardiovasc Med. 2008 Jan;5(1):22-9. doi: 10.1038/ncpcardio1066.
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