Gao Yue, Erickson Alan R, Pipinos Iraklis I, Garg Nitin
Division of Vascular Surgery, Department of Surgery, University of Nebraska Medical Center, Omaha, Neb.
Division of Rheumatology, Department of Internal Medicine, University of Nebraska Medical Center, Omaha, Neb.
J Vasc Surg Cases Innov Tech. 2019 Apr 28;5(2):95-98. doi: 10.1016/j.jvscit.2018.10.003. eCollection 2019 Jun.
Idiopathic aortitis is an inflammatory disease of the aorta that is diagnosed after the less frequent infectious and rheumatologic variants are excluded. The etiology and natural history of the disease are poorly understood, and its presentation is variable; the need for exclusion of infectious, malignant, and rheumatologic causes can make its evaluation and diagnosis challenging. Treatment is tailored to the diagnosis and may include observation, antimicrobial therapies, and immunosuppressive agents when appropriate. Operative therapy is rarely needed and reserved for symptomatic patients or instances in which infection cannot be excluded. We present a case of idiopathic aortitis that resolved spontaneously with expectant management and discuss the pitfalls in the diagnosis and care of the disease.
特发性主动脉炎是一种主动脉的炎症性疾病,在排除了较少见的感染性和风湿性变体后得以诊断。该疾病的病因和自然史了解甚少,其表现各异;需要排除感染、恶性和风湿性病因,这使得其评估和诊断具有挑战性。治疗根据诊断进行调整,可能包括观察、抗菌治疗以及在适当情况下使用免疫抑制剂。手术治疗很少需要,仅适用于有症状的患者或无法排除感染的情况。我们报告一例特发性主动脉炎患者,通过期待治疗自发缓解,并讨论该疾病诊断和治疗中的陷阱。