Joseph Anne D D, Pradeepan Jebananthy Anandaselvam, Kumanan Thirunavukarasu, Malaravan Muthusamy
University Medical Unit, Teaching Hospital Jaffna, Jaffna, Sri Lanka.
Department of Ophthalmology, Teaching Hospital Jaffna, Jaffna, Sri Lanka.
Case Rep Rheumatol. 2019 Sep 22;2019:3236821. doi: 10.1155/2019/3236821. eCollection 2019.
Giant cell arteritis, a large vessel vasculitis is characterized by headache, visual impairment, constitutional symptoms, and increased inflammatory markers. Visual involvement in giant cell arteritis ranges from amaurosis fugax to permanent visual loss, and extensive bilateral visual impairment is a rare presentation. We hereby report a case of combined left central retinal artery occlusion and bilateral anterior ischemic optic neuritis in a patient who poorly responded to standard corticosteroid therapy.
巨细胞动脉炎是一种大血管血管炎,其特征为头痛、视力损害、全身症状以及炎症标志物升高。巨细胞动脉炎的视力受累范围从一过性黑矇到永久性视力丧失,双侧广泛视力损害是一种罕见的表现。我们在此报告一例患者,其合并左侧视网膜中央动脉阻塞和双侧前部缺血性视神经炎,对标准皮质类固醇治疗反应不佳。