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[两例儿童膀胱横纹肌肉瘤]

[Two cases of rhabdomyosarcoma of the bladder in children].

作者信息

Tanaka Y, Kawauchi A, Kitamori T, Imada N, Ohne T, Watanabe H

机构信息

Department of Urology, Kyoto Prefectural University of Medicine.

出版信息

Hinyokika Kiyo. 1995 Jul;41(7):549-51.

PMID:7668188
Abstract

A 1-year-old boy was admitted to our hospital with chief complaint of urinary retention and a lower abdominal large mass. The mass was shown in the bladder by computerized tomography (CT) associated with paraaortic lymph node swelling. Tumor biopsy revealed rhabdomyosarcoma, embryonal type. Complete remission (CR) was obtained by chemotherapy based on STS' 88. He has been healthy 40 months without recurrence. A similar case of rhabdomyosarcoma, embryonal type, in the bladder in a 3-year-old girl with a chief complaint of macrohematuria was verified by CT and tumor biopsy. The same chemotherapy was performed, resulting in partial remission (PR). A complete resection of the tumor was achieved by partial cystectomy. She is alive without recurrence 18 months after the cystectomy.

摘要

一名1岁男童因尿潴留和下腹部巨大肿块为主诉入院。计算机断层扫描(CT)显示肿块位于膀胱,并伴有主动脉旁淋巴结肿大。肿瘤活检显示为胚胎型横纹肌肉瘤。基于STS' 88方案的化疗使患儿获得完全缓解(CR)。他已健康40个月,无复发。一名3岁女童因肉眼血尿为主诉,经CT和肿瘤活检证实膀胱内有一例类似的胚胎型横纹肌肉瘤。采用相同化疗方案,结果为部分缓解(PR)。通过部分膀胱切除术实现了肿瘤的完全切除。膀胱切除术后18个月,她仍存活,无复发。

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