Ghareeb Amjad, Kakaje Ameer, Ghareeb Ayham, Nahas Mohamad Ali
Damascus University, Faculty of Medicine, Damascus, Syria.
Damascus University, Faculty of Medicine, Damascus, Syria.
Int J Surg Case Rep. 2020;71:244-249. doi: 10.1016/j.ijscr.2020.05.010. Epub 2020 May 23.
Arteriovenous malformations (AVMs) are rare congenital lesions that affect multiple regions. AVMs often affect the brain and the buttock is the least common. They are usually congenital, but discovered later in life as they are asymptomatic, small and resemble a benign lesion. However, they can abruptly grow and become symptomatic and life-threatening as they can bleed and get infected.
An eight-year-old girl presented with ulcerated and bleeding AVM at the sacro gluteal region. However, due to financial difficulty, it grew to reach an enormous size of (15152 cm) in the buttock. It was later managed by multiple embolisation followed by total surgical resection.
This case reflects the first case of enormous AVM in the sacro-gluteal region in a child in the Middle East as they rarely reach such huge sizes. Total resection was possible by repeat embolisation and surgery.
Embolisation can render even huge AVM operable. AVMs should be treated as early as possible as they continue to grow and drastically decrease the quality of life of the patient.
动静脉畸形（AVM）是一种罕见的先天性病变，可累及多个部位。AVM常累及脑部，而累及臀部最为少见。它们通常是先天性的，但由于无症状、体积小且类似良性病变，常在生命后期才被发现。然而，它们可能会突然增大并出现症状，甚至危及生命，因为它们可能出血和感染。
一名8岁女孩骶臀区域出现溃疡出血性AVM。然而，由于经济困难，其在臀部发展到巨大尺寸（15×15×2厘米）。随后通过多次栓塞治疗，继而进行了完整的手术切除。
该病例是中东地区首例儿童骶臀区域巨大AVM，因为它们很少发展到如此巨大的尺寸。通过重复栓塞和手术实现了完整切除。
栓塞治疗可使巨大AVM得以手术切除。AVM应尽早治疗，因为它们会持续生长并严重降低患者的生活质量。
