Yüksel Cabir, Kocaman Gökhan, Yenigün Bülent Mustafa, Özakıncı Hilal, Dizbay Sak Serpil, Enön Serkan, Kutlay Hakan
Department of Thoracic Surgery, Ankara University School of Medicine, Ankara, Turkey.
Department of Medical Pathology, Ankara University School of Medicine, Ankara, Turkey.
Turk Gogus Kalp Damar Cerrahisi Derg. 2020 Apr 22;28(2):394-398. doi: 10.5606/tgkdc.dergisi.2020.18844. eCollection 2019 Jun.
Paraganglioma is a rare tumor originating from extra-adrenal chromaffin cells. Primary pulmonary paraganglioma can also be seen in pediatric patients. Due to its endobronchial localization, morphological features, and neuroendocrine immunohistochemical profile, primary pulmonary paraganglioma can be confused with carcinoid tumor. Primary pulmonary paraganglioma should be considered in the differential diagnosis of endobronchial tumors and necessary precautions should be taken, considering that it may be functioning. In appropriate cases, bronchial sleeve resection provides curative treatment. In this article, we present two cases: First was a functioning primary pulmonary paraganglioma that underwent lobectomy and second was an entirely endobronchial tumor without any extra-bronchial spread that underwent bronchial sleeve resection.
副神经节瘤是一种起源于肾上腺外嗜铬细胞的罕见肿瘤。原发性肺副神经节瘤也可见于儿科患者。由于其支气管内定位、形态特征和神经内分泌免疫组化特征，原发性肺副神经节瘤可能与类癌肿瘤混淆。在支气管内肿瘤的鉴别诊断中应考虑原发性肺副神经节瘤，并应采取必要的预防措施，因为它可能具有功能。在适当的情况下，支气管袖状切除术可提供根治性治疗。在本文中，我们介绍两例病例：第一例是接受肺叶切除术的功能性原发性肺副神经节瘤，第二例是未发生任何支气管外扩散的完全位于支气管内的肿瘤，接受了支气管袖状切除术。
