Geoffrion Tracy R, DeKeyzer Linde, Shah Gopi, Nair Suja J, Pirolli Timothy J, Kernstine Kemp
Department of Cardiovascular and Thoracic Surgery, University of Texas Southwestern Medical Center, Dallas, TX, USA.
Department of Pulmonary Medicine, University of Texas Southwestern Medical Center, Dallas, TX, USA.
J Surg Case Rep. 2018 Apr 3;2018(4):rjy047. doi: 10.1093/jscr/rjy047. eCollection 2018 Apr.
Paraganglioma is a rare extra-adrenal tumor of the paraganglia often found in association with sympathetic and parasympathetic nerves. The case presented is of a 10-year-old boy with hemoptysis who was found to have an obstructive bronchial mass. He underwent surgical resection and biopsy confirmed primary pulmonary paraganglioma. He was subsequently found to have an associated genetic syndrome. This is the first case report describing a primary pulmonary paraganglioma in a child.
副神经节瘤是一种罕见的肾上腺外副神经节肿瘤，常与交感神经和副交感神经相关。所呈现的病例是一名10岁咯血男孩，发现有阻塞性支气管肿块。他接受了手术切除，活检证实为原发性肺副神经节瘤。随后发现他患有相关的遗传综合征。这是第一例描述儿童原发性肺副神经节瘤的病例报告。
