Hakim Ikram, Yunus Mohd Razif Mohamad
Universiti Kebangsaan Malaysia Medical Center, Department of Otorhinolaryngology and Head and Neck Surgery, Kuala Lumpur, Malaysia.
Medeni Med J. 2020;35(3):271-275. doi: 10.5222/MMJ.2020.88120. Epub 2020 Sep 30.
Histopathologically adult extracardiac rhabdomyoma is a benign tumour of mature striated muscle. It is a slow- growing tumour with predilection to occur in head and neck region. They appear mainly as a solitary lesion, and about 15% of them can be multicentric. A 56-year-old man presented to us with the floor of mouth swelling persisted for one year and the right neck swelling for three years mimicking a plunging ranula. Radiological imaging revealed enhancing mass at the floor of mouth and submandibular region. The mass represented a nonvascular benign tumour. Subsequently, the patient underwent excision of the mass via transcervical and transoral method. Histopathological examination revealed adult type of extracardiac rhabdomyoma. Adult type of extracardiac rhabdomyoma should be considered in the differential diagnosis for the head and neck masses. A complete excision will reduce the risk of recurrence.
组织病理学上,成人心脏外横纹肌瘤是一种成熟横纹肌的良性肿瘤。它是一种生长缓慢的肿瘤,好发于头颈部区域。它们主要表现为单个病灶,约15%可为多中心性。一名56岁男性因口底肿胀持续一年、右颈部肿胀三年前来就诊,疑似舌下囊肿。影像学检查显示口底和下颌下区域有强化肿块。该肿块为非血管性良性肿瘤。随后,患者通过经颈和经口方法切除了肿块。组织病理学检查显示为成人型心脏外横纹肌瘤。头颈部肿块的鉴别诊断应考虑成人型心脏外横纹肌瘤。完整切除可降低复发风险。