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胰岛素自身免疫综合征——病例系列

Insulin Autoimmune Syndrome - A Case Series.

作者信息

Boro Hiya, Gupta Uttio, Singh Charandeep, Malhotra Rakhi, Khadgawat Rajesh

机构信息

Department of Endocrinology and Metabolism, All India Institute of Medical Sciences, New Delhi, India.

出版信息

Eur Endocrinol. 2020 Oct;16(2):168-171. doi: 10.17925/EE.2020.16.2.168. Epub 2020 Oct 6.

DOI:10.17925/EE.2020.16.2.168
PMID:33117451
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7572167/
Abstract

Insulin autoimmune syndrome, or Hirata's disease, is a rare cause of hypoglycaemia. It is characterised by spontaneous episodes of hypoglycaemia, without any exposure to exogenous insulin. The majority of cases are seen in the Japanese population and it is rarely found to affect other ethnicities. The recognition of this disease is important to avoid unnecessary investigations and procedures. Here, we report two cases of insulin autoimmune syndrome, which were diagnosed and managed in our institute.

摘要

胰岛素自身免疫综合征,即平田病,是低血糖症的一种罕见病因。其特征为自发性低血糖发作,且未接触任何外源性胰岛素。大多数病例见于日本人群,很少发现会影响其他种族。认识这种疾病对于避免不必要的检查和程序很重要。在此,我们报告在我院诊断和治疗的两例胰岛素自身免疫综合征病例。

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引用本文的文献

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本文引用的文献

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Clin Endocrinol (Oxf). 2020 May;92(5):409-420. doi: 10.1111/cen.14174. Epub 2020 Feb 26.
2
Insulin Autoantibody Syndrome: Varying Clinical Presentations and Response Patterns of an Underrecognized Entity.胰岛素自身抗体综合征:一种未被充分认识的疾病的多样临床表现及反应模式
Indian J Endocrinol Metab. 2019 Sep-Oct;23(5):540-544. doi: 10.4103/ijem.IJEM_335_19.
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Autoimmune Hypoglycemia Relapse on Glucocorticoids, Effectively Treated with Azathioprine.自身免疫性低血糖在糖皮质激素治疗后复发,硫唑嘌呤有效治疗
J Assoc Physicians India. 2018 Dec;66(12):78-79.
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Rituximab for treatment of refractory insulin autoimmune syndrome associated with non-Hodgkin B-cell lymphoma.利妥昔单抗治疗与非霍奇金B细胞淋巴瘤相关的难治性胰岛素自身免疫综合征。
Clin Endocrinol (Oxf). 2019 Jul;91(1):230-232. doi: 10.1111/cen.13998. Epub 2019 May 14.
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Spontaneously remitting insulin autoimmune syndrome in a patient taking alpha-lipoic acid.一名服用α-硫辛酸的患者出现自发缓解的胰岛素自身免疫综合征。
Endocrinol Diabetes Metab Case Rep. 2018;2018. doi: 10.1530/EDM-18-0122. Epub 2018 Dec 11.
6
Insulin autoimmune syndrome: from diagnosis to clinical management.胰岛素自身免疫综合征:从诊断到临床管理
Ann Transl Med. 2018 Sep;6(17):335. doi: 10.21037/atm.2018.07.32.
7
Immunoadsorption Followed by Rituximab as a Definitive Treatment for Insulin Autoimmune Syndrome (Hirata Syndrome): A Case Report.免疫吸附继以利妥昔单抗作为胰岛素自身免疫综合征(平田综合征)的确定性治疗:一例报告
Diabetes Care. 2018 Mar;41(3):e23-e24. doi: 10.2337/dc17-1974. Epub 2017 Dec 27.
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"Riding High on Low Fuel" - Our Experience with Endogenous Hyperinsulinemic Hypoglycemia.“低燃料下的高骑行”——我们关于内源性高胰岛素血症性低血糖症的经验
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