Watanabe Yukina, Yamamoto Miyuki, Igari Syohei, Yamamoto Toshiyuki
Department of Dermatology, Fukushima Medical University, Fukushima, Japan.
Indian Dermatol Online J. 2020 Nov 8;11(6):979-982. doi: 10.4103/idoj.IDOJ_46_20. eCollection 2020 Nov-Dec.
Wells syndrome or eosinophilic cellulitis is an idiopathic inflammatory dermatitis characterized by a benign but recurrent evolution. It often causes edematous urticarial plaques on the extremities. Herein, we report two rare cases of Wells syndrome with marked swelling in the hands. Both cases exhibited various clinical features. Case 1 was Wells syndrome with collagen disease-like sclerotic edema in the fingers and annular erythema on the trunk. Case 2 was Wells syndrome with diffuse plate-like hardening of the forearm mimicking cellulitis, which required fasciotomy due to suspected compartment syndrome at the emergency room. Wells syndrome should be included in the differential diagnosis of patients presenting with marked diffuse swelling in the hands.
韦尔斯综合征或嗜酸性粒细胞性蜂窝织炎是一种特发性炎症性皮肤病,其特征为良性但反复发作。它常导致四肢出现水肿性荨麻疹斑块。在此,我们报告两例罕见的手部明显肿胀的韦尔斯综合征病例。两例均表现出各种临床特征。病例1为韦尔斯综合征,手指出现类似胶原病的硬化性水肿,躯干出现环状红斑。病例2为韦尔斯综合征,前臂弥漫性板状硬化,类似蜂窝织炎,因急诊室怀疑骨筋膜室综合征而需要进行筋膜切开术。对于手部出现明显弥漫性肿胀的患者,鉴别诊断时应考虑韦尔斯综合征。