Cotella Juan I, Dantur Julio, Hasbani Eduardo, Hasbani Javier, Mayor Marcela Ortiz, Prado Aldo
Centro Privado De Cardiología, Tucumán, Argentina.
J Cardiovasc Echogr. 2020 Jul-Sep;30(3):179-182. doi: 10.4103/jcecho.jcecho_87_20. Epub 2020 Nov 9.
Relapsing polychondritis (RP) is a rare multisystem disease characterized by inflammation in cartilaginous structures and other connective tissues throughout the body, affecting the ears, nose, eyes, joints, respiratory tract, heart, and blood vessels. Cardiovascular involvement is the second most common cause of mortality after laryngotracheal involvement.[1] Here, we report a successful surgical case of RP in which the patient underwent aortic and mitral valve replacement and concomitant coronary artery bypass grafting.
复发性多软骨炎(RP)是一种罕见的多系统疾病,其特征是全身软骨结构和其他结缔组织发生炎症,影响耳朵、鼻子、眼睛、关节、呼吸道、心脏和血管。心血管受累是继喉气管受累后第二常见的死亡原因。[1] 在此,我们报告一例RP的成功手术病例,该患者接受了主动脉瓣和二尖瓣置换术以及同期冠状动脉旁路移植术。