Bhamra Kuljeet, Weerasinghe Rachel, Steuer Alan
Department of Rheumatology, Heatherwood and Wexham Park Hospitals NHS Foundation Trust, Slough, Berkshire SL2 4HL, UK.
Case Rep Rheumatol. 2011;2011:726038. doi: 10.1155/2011/726038. Epub 2012 Jan 4.
Relapsing polychondritis (RP) is a rare multisystem disease. It is characterized by recurrent inflammation of cartilaginous structures including the ears, nose, tracheo-bronchial tree and peripheral joints. Proteoglycan-rich structures such as the heart, eyes and blood vessels can also be affected. Systemic symptoms including fever, weight loss and lethargy are common. RP is difficult to diagnose as it presents in a wide variety of ways and there is no diagnostic test. Corticosteroids are the mainstay of treatment but other immunosuppressive drugs can be used in combination with steroids. We present an unusual presentation of RP.
复发性多软骨炎（RP）是一种罕见的多系统疾病。其特征是包括耳朵、鼻子、气管支气管树和外周关节在内的软骨结构反复发炎。富含蛋白聚糖的结构，如心脏、眼睛和血管也可能受到影响。常见的全身症状包括发热、体重减轻和乏力。RP难以诊断，因为其表现形式多种多样且没有诊断性检查。皮质类固醇是主要的治疗药物，但其他免疫抑制药物可与类固醇联合使用。我们报告一例RP的不寻常表现。
