Samà Laura, Tzanis Dimitri, Bouhadiba Toufik, Bonvalot Sylvie
Sarcoma, Melanoma and Rare Tumors Surgery Unit, Humanitas Clinical and Research Center - IRCCS, MIlan, ITA.
Department of Biomedical Sciences, Humanitas University, Milan, ITA.
Cureus. 2021 Mar 17;13(3):e13936. doi: 10.7759/cureus.13936.
Retroperitoneal sarcoma (RPS) is a rare and heterogeneous tumor. A percutaneous core needle biopsy (PCNB) is required for obtaining a histological diagnosis of the condition and for planning the therapy. Surgery is the standard of care for RPS; it is a standardized procedure, and it should be performed in a referral sarcoma center. Sarcoma surgery is rarely performed on an urgent or emergent basis. In this report, we describe a case of a retroperitoneal leiomyosarcoma that presented with spontaneous rupture and hemoperitoneum, which required surgical treatment in an urgent manner. To our knowledge, this is the first case of hemoperitoneum due to RPS rupture to be reported in the literature.
腹膜后肉瘤（RPS）是一种罕见的异质性肿瘤。获取该疾病的组织学诊断以及制定治疗方案都需要进行经皮穿刺活检（PCNB）。手术是RPS的标准治疗方法；它是一种标准化程序，应在肉瘤转诊中心进行。肉瘤手术很少在紧急情况下进行。在本报告中，我们描述了一例腹膜后平滑肌肉瘤患者，该患者出现自发性破裂和腹腔积血，需要紧急进行手术治疗。据我们所知，这是文献中首次报道因RPS破裂导致腹腔积血的病例。
