Margaretha Puspita Ayu, Rusmawatiningtyas Desy, Makrufardi Firdian, Kumara Intan Fatah
Department of Child Health, Faculty of Medicine, Public Health and Nursing, Universitas Gadjah Mada/Dr. Sardjito Hospital, Yogyakarta, 55281, Indonesia.
Ann Med Surg (Lond). 2021 Jul 28;68:102614. doi: 10.1016/j.amsu.2021.102614. eCollection 2021 Aug.
and importance: Congenital cystic adenomatoid malformation (CCAM) is a rare cystic lesion in the lungs. CCAM might present in the early neonatal period with symptoms of respiratory distress.
A 2-year-old girl was admitted to our Pediatric Intensive Care Unit with signs of severe respiratory distress. She had been diagnosed with CCAM since she was three months old. She also had undergone several procedures such as thoracotomy and decortication since then, but she still suffered some episodes of pulmonary infection. In this admission, her computerized thoracic tomography revealed a pleuropulmonary blastoma (PPB).
An obstruction of blood outflow from the left ventricle could happen when an intrathoracic mass exists, leading to a decrease of cardiac output and resulting in an obstructive shock, which could be fatal. One of the malignancy types commonly occurring is pleuropulmonary blastoma (PPB), which has a poor prognosis. Early detection on CCAM can be done by prenatal ultrasound.
Obstructive shock is one of complication that might occur in pleuropulmonary blastoma.
及重要性：先天性囊性腺瘤样畸形（CCAM）是肺部一种罕见的囊性病变。CCAM可能在新生儿早期出现呼吸窘迫症状。
一名2岁女孩因严重呼吸窘迫体征入住我们的儿科重症监护病房。她自3个月大时就被诊断为CCAM。从那时起，她还接受了诸如开胸手术和剥脱术等多项手术，但仍有几次肺部感染发作。在此次入院时，她的胸部计算机断层扫描显示为胸膜肺母细胞瘤（PPB）。
当胸腔内存在肿块时，可能会发生左心室血液流出受阻，导致心输出量减少并引发梗阻性休克，这可能是致命的。常见的恶性肿瘤类型之一是胸膜肺母细胞瘤（PPB），其预后较差。CCAM的早期检测可通过产前超声进行。
梗阻性休克是胸膜肺母细胞瘤可能发生的并发症之一。
