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不宁臂综合征:一种罕见病?

Restless arm syndrome: a rare disease?

机构信息

Bayerische Ärztekammer München, D-81677 München, Bavaria, Germany

Bayerische Ärztekammer München, D-81677 München, Bavaria, Germany.

出版信息

BMJ Case Rep. 2021 Sep 20;14(9):e244890. doi: 10.1136/bcr-2021-244890.

Abstract

Restless legs syndrome (RLS) is a common neurological disorder characterised by an irresistible urge to move the lower limbs, often accompanied by unpleasant sensations in the legs, typically occurring in the evening and at night and improving with movement. Restless arms syndrome (RAS) predominantly affects the arms, while the legs are rarely affected. RAS appears to be very rare, with very few cases described to date, but the diagnosis of RAS is probably made too infrequently, especially for milder and transient forms. The patient reported here even had severe symptoms for years that could have indicated RAS. He observed an immediate improvement in all RAS-related symptoms after administration of 100 mg L-dopa +25 mg benserazide, which continues to this day. Clinicians should always be alert for RLS-like symptoms in one or both arms that worsen at rest and improve with movement, thinking of possible RAS.

摘要

不宁腿综合征(RLS)是一种常见的神经系统疾病,其特征是下肢不可抑制地移动,常伴有腿部不适感觉,通常在傍晚和夜间发生,活动后可改善。不宁臂综合征(RAS)主要影响手臂,腿部很少受累。RAS 似乎非常罕见,迄今为止描述的病例很少,但 RAS 的诊断可能过于频繁,尤其是对于较轻和短暂的病例。这里报告的患者甚至多年来一直有严重的症状,这些症状可能表明存在 RAS。他观察到在服用 100mg L-多巴+25mg 卡比多巴后,所有与 RAS 相关的症状立即改善,这种情况持续至今。临床医生应始终警惕单侧或双侧手臂出现类似于 RLS 的症状,即休息时加重、活动时改善,同时考虑可能存在 RAS。

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