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表现为肝硬化伴门静脉高压的肺外结节病

Extrapulmonary Sarcoidosis Manifested as Cirrhosis with Portal Hypertension.

作者信息

Kothakota Sunil Raviraj, Kumar Nair Ajith, Sasidharan Madhu, Kareem Harish, Praveen Kumar C, Kanala Jagadeswarareddy

机构信息

Senior Resident, Kerala Institute of Medical Sciences, Kerala, India.

Department of Medical Sciences, Kerala Institute of Medical Sciences, Kerala, India.

出版信息

Middle East J Dig Dis. 2021 Apr;13(2):160-162. doi: 10.34172/mejdd.2021.220. Epub 2021 May 29.

DOI:10.34172/mejdd.2021.220
PMID:34712455
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8531926/
Abstract

Hepatic involvement has been reported in 20-30% of patients with systemic sarcoidosis. However, isolated liver involvement is rare. We report a case of cirrhosis with portal hypertension, diagnosed as hepatic sarcoidosis based on high angiotensin-converting enzyme level and presence of multiple non-caseating granulomas in liver histopathology. She improved clinically after treatment with steroid and ursodeoxycholic acid.

摘要

据报道，20%-30%的系统性结节病患者会出现肝脏受累。然而，孤立性肝脏受累情况罕见。我们报告一例伴有门静脉高压的肝硬化病例，根据高血管紧张素转换酶水平以及肝脏组织病理学中存在多个非干酪样肉芽肿，诊断为肝结节病。经类固醇和熊去氧胆酸治疗后，她的临床症状有所改善。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6f56/8531926/99f7262fbcad/mejdd-13-160-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6f56/8531926/3cd2de304b8d/mejdd-13-160-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6f56/8531926/99f7262fbcad/mejdd-13-160-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6f56/8531926/3cd2de304b8d/mejdd-13-160-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6f56/8531926/99f7262fbcad/mejdd-13-160-g002.jpg

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