Aldabbab Habib Y, Hakeem Moayad A, Alanazi Fatimah M, Asiri Mohammed A, Al Hani Mohammad F, Alshareef Rahaf I, Alkahtani Abeer R, Alfadhli Rahaf F, Alharbi Lama Y, Jan Abdulla A, Alraddadi Mohanned M, Alshammari Malak
College of Medicine, King Faisal University, Al-Ahsa, SAU.
College of Medicine, University of Jeddah, Jeddah, SAU.
Cureus. 2021 Oct 7;13(10):e18560. doi: 10.7759/cureus.18560. eCollection 2021 Oct.
Polycystic liver disease is a rare clinical condition that causes portal hypertension. It constitutes a group of disorders with liver lesions resulting from abnormal development of the embryological ductal system. Isolated polycystic disease with the absence of polycystic kidney disease is considered a rare condition. We present the case of a 46-year-old man who presented with epigastric pain and episodes of hematemesis. Abdominal examination revealed enlarged liver. He underwent a computed tomography scan that revealed innumerable cystic liver lesions with the presence of ascites. Further investigations confirmed abnormal liver functions and portal hypertension. Physicians need to consider this diagnosis in the appropriate clinical settings. Extensive involvement of the liver may lead to persistent severe symptoms requiring liver transplantation.
多囊肝病是一种导致门静脉高压的罕见临床病症。它是一组因胚胎导管系统发育异常而导致肝脏病变的疾病。孤立性多囊病且无多囊肾病被认为是一种罕见病症。我们报告一例46岁男性病例，该患者出现上腹部疼痛和呕血症状。腹部检查发现肝脏肿大。他接受了计算机断层扫描，结果显示肝脏有无数囊性病变且伴有腹水。进一步检查证实肝功能异常和门静脉高压。医生在适当的临床情况下需要考虑这一诊断。肝脏的广泛受累可能导致持续的严重症状，需要进行肝移植。
