Dańczak-Pazdrowska Aleksandra, Cieplewicz Paulina, Żaba Ryszard, Adamski Zygmunt, Polańska Adriana
Department of Dermatology, Poznan University of Medical Sciences, Poznan, Poland.
Department of Dermatology and Venereology, Poznan University of Medical Sciences, Poznan, Poland.
Postepy Dermatol Alergol. 2021 Oct;38(5):716-720. doi: 10.5114/ada.2021.106242. Epub 2021 May 18.
Morphea, also known as localized scleroderma, is a chronic, autoimmune disease of connective tissue. It is characterized by a typical clinical feature. In morphea, there is no Raynaud's phenomenon, no sclerodactyly or no ulcerations on the fingertips. Although morphea and systemic sclerosis have been perceived as separate disease entities for years, they are still confused both by patients (which is a source of unnecessary stress) and doctors. This may be due to, in part, misunderstood terminology. The controversy around morphea also concerns the division of this disease entity, including its less common subtypes, such as eosinophilic fasciitis. Discussions also revolve around the diagnostic aspects and possible treatment options. The paper attempts to present the debatable aspects regarding nomenclature, classification, diagnosis and treatment of morphea.
硬斑病，也称为局限性硬皮病，是一种慢性结缔组织自身免疫性疾病。它具有典型的临床特征。在硬斑病中，不存在雷诺现象、指端硬化或指尖溃疡。尽管多年来硬斑病和系统性硬化症一直被视为不同的疾病实体，但患者（这是不必要压力的来源）和医生仍会将它们混淆。这在一定程度上可能是由于术语误解。围绕硬斑病的争议还涉及该疾病实体的划分，包括其不太常见的亚型，如嗜酸性筋膜炎。讨论也围绕诊断方面和可能的治疗选择展开。本文试图阐述关于硬斑病命名、分类、诊断和治疗的争议点。
