Thippeswamy Pushpa B, Soundararajan Dilip C R, Kanna Ríshi M, Kuna Venkata S, Rajasekaran Shanmuganathan
Department of Radiology, Ganga Hospital, Coimbatore, Tamil Nadu, India.
Department of Spine Surgery, Ganga Hospital, Coimbatore, Tamil Nadu, India.
Indian J Radiol Imaging. 2022 Jan 10;31(4):1057-1061. doi: 10.1055/s-0041-1741047. eCollection 2021 Oct.
Cauda equina intradural tumors commonly reported include ependymoma, schwannoma, neurofibroma, meningioma, and drop metastasis. Hemangioblastoma of the neural axis is a rare benign vascular tumor comprising only 1.6 to 6.4% of spinal tumors, and are usually associated with Von-Hippel Lindau disease. Sporadic intradural extramedullary hemangioblastoma involving cauda equina is very rare with only countable reports, and the presence of peritumoral cyst has been reported only once. We report one such case of hemangioblastoma with a large peritumoral cyst, which was diagnosed radiologically and confirmed by histopathology following surgical excision. Pertinent radiological characteristics, diagnostic clues, treatment, and surgical outcomes are discussed.
常见的马尾硬膜内肿瘤包括室管膜瘤、神经鞘瘤、神经纤维瘤、脑膜瘤和转移瘤。神经轴母细胞瘤是一种罕见的良性血管肿瘤，仅占脊柱肿瘤的1.6%至6.4%，通常与冯-希佩尔-林道病相关。散发性累及马尾的硬膜内髓外母细胞瘤非常罕见，仅有少数病例报道，且瘤周囊肿的存在仅被报道过一次。我们报告了一例伴有巨大瘤周囊肿的母细胞瘤病例，该病例经放射学诊断，并在手术切除后经组织病理学证实。文中讨论了相关的放射学特征、诊断线索、治疗方法及手术结果。
