Department of Surgery, Nepal Medical College and Teaching Hospital, Attarkhel, Kathmandu, Nepal.
Department of Pathology, Kathmandu Medical College and Teaching Hospital, Sinamangal, Kathmandu, Nepal.
JNMA J Nepal Med Assoc. 2021 Sep 11;59(241):919-921. doi: 10.31729/jnma.6516.
Desmoid tumors most commonly occur in the anterior abdominal wall in approximately 50% of cases and are locally aggressive. We describe a case of a 38-year-old lady who was investigated as a case of gastrointestinal tumor. Post-operative immunohistochemistry staining showed the presence of a synchronous desmoid in the abdominal wall and proximal ileum. Wide local excision remains the gold-standard of treatment with pharmacotherapeutics and radiotherapy serving as adjuvant or palliative treatment options.
纤维瘤病最常发生在前腹壁,约占 50%病例,且具有局部侵袭性。我们描述了一例 38 岁女性,她被诊断为胃肠道肿瘤。术后免疫组化染色显示腹壁和回肠近端存在同步纤维瘤病。广泛局部切除仍然是治疗的金标准,药物治疗和放射治疗作为辅助或姑息治疗选择。