掌跖角化病：少汗性外胚层发育不良的一种不寻常表现。

Abdelli Wissal, Souissi Asmahen, Alaoui Fatima, Sassi Wiem, Chelly Ines, Haouat Slim, Mokni Mourad

Dermatology Department - Rabta hospital Tunis Tunisia.

Anatomopathology department-Rabta hospital Tunis Tunisia.

Clin Case Rep. 2022 Mar 13;10(3):e05577. doi: 10.1002/ccr3.5577. eCollection 2022 Mar.

Rapp-Hodgkin syndrome (RHS) is a rare condition that is characterized by ectodermal dysplasia and palatal abnormalities. Palmoplantar keratoderma (PPK) is an unusual manifestation of hidrotic ED. Ulcerations on the palms are also not common in RHS. We describe a 15-year-old boy who has RHS associated with PPK.

拉普-霍奇金综合征（RHS）是一种罕见疾病，其特征为外胚层发育异常和腭部畸形。掌跖角化病（PPK）是多汗性外胚层发育不良的一种不寻常表现。手掌溃疡在RHS中也不常见。我们描述了一名患有RHS并伴有PPK的15岁男孩。