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新生儿先天性袋状结肠

Congenital Pouch Colon in a Neonate.

作者信息

Niaz Sana, Naz Sahira, Raziq Rumaissa Abdul

机构信息

Sana Niaz, MBBS, FCPS, Department of Neonatology, Indus Hospital & Health Network, Karachi, Pakistan.

Sahira Naz, MBBS, FCPS, Department of Pediatrics, Indus Hospital & Health Network, Karachi, Pakistan.

出版信息

Pak J Med Sci. 2022 Jan;38(2):426-429. doi: 10.12669/pjms.38.ICON-2022.5771.

DOI:10.12669/pjms.38.ICON-2022.5771
PMID:35310792
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC8899889/
Abstract

Congenital Pouch Colon (CPC) is a rare anorectal malformation (ARM) in which a part of or the entire colon is replaced by pouch-like dilatation. Males are more likely to be diagnosed with the condition compared to females. The highest incidence of the disease is in South Asia, with a significant number of cases reported from India. Early diagnosis can be made when there are hypoechogenic lesions on antenatal ultrasound scans. We report a case of a neonate with routine antenatal scans who presented with a distended abdomen and inability to pass feces. The diagnosis was made in the early neonatal period, followed by surgical management.

摘要

先天性袋状结肠(CPC)是一种罕见的肛肠畸形(ARM),其中部分或整个结肠被袋状扩张所取代。与女性相比,男性更易被诊断出患有此病。该疾病在南亚发病率最高,印度报告了大量病例。当产前超声扫描出现低回声病变时可作出早期诊断。我们报告一例新生儿病例,该患儿在常规产前扫描时被发现,出生后出现腹部膨隆且无法排便。在新生儿早期作出诊断,随后进行了手术治疗。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c9dc/8899889/d7326dbee865/PJMS-38-426-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c9dc/8899889/28db65f418a2/PJMS-38-426-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c9dc/8899889/c09c13f61c76/PJMS-38-426-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c9dc/8899889/d7326dbee865/PJMS-38-426-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c9dc/8899889/28db65f418a2/PJMS-38-426-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c9dc/8899889/c09c13f61c76/PJMS-38-426-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/c9dc/8899889/d7326dbee865/PJMS-38-426-g003.jpg

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Congenital Pouch Colon in a Neonate.新生儿先天性袋状结肠
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本文引用的文献

1
Congenital Pouch Colon.先天性袋状结肠
J Indian Assoc Pediatr Surg. 2017 Apr-Jun;22(2):69-78. doi: 10.4103/jiaps.JIAPS_5_17.
2
Congenital pouch colon: a preliminary report from pakistan.先天性袋状结肠:来自巴基斯坦的初步报告。
J Neonatal Surg. 2012 Jul 1;1(3):37. eCollection 2012 Jul-Sep.
3
Management of congenital pouch colon based on the Saxena-Mathur classification.基于萨克森纳-马图尔分类法的先天性袋状结肠的管理
J Pediatr Surg. 2009 May;44(5):962-6. doi: 10.1016/j.jpedsurg.2009.01.035.
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Congenital pouch colon revisited.先天性袋状结肠再探讨。
J Pediatr Surg. 1998 Oct;33(10):1510-5. doi: 10.1016/s0022-3468(98)90487-0.
5
Congenital short colon.先天性短结肠
World J Surg. 1996 Jan;20(1):107-14. doi: 10.1007/s002689900019.