Alshehri Saleh Saad, Minhaji Bushra Iftekhar, Pasha Mohsina Reshma
King Saud Medical City, Riyadh, Saudi Arabia.
SAGE Open Med Case Rep. 2022 Mar 22;10:2050313X221086814. doi: 10.1177/2050313X221086814. eCollection 2022.
Idiopathic hypereosinophilic syndrome in children is a rare disease. Even with improved understanding of eosinophilic disorders and recent advances in diagnostic modalities, evaluation of hypereosinophilia remains challenging due to heterogeneous etiologic factors. In acute clinical settings, the management plan is often unclear as the condition is not encountered frequently. It is often associated with leucocytosis, but hyperleucocytosis causing multiorgan dysfunction in the absence of malignancy is rarely seen. A previously well 5-year-old boy presented to our emergency room with a 2-week history of fever, progressive cough and dyspnoea, rapidly progressing to respiratory failure and acute respiratory distress syndrome. Hyperleucocytosis with hypereosinophilia on peripheral blood film, bilateral pulmonary infiltrates on X-ray and ground glass opacities suggested hypereosinophilic syndrome with secondary acute respiratory distress syndrome. Owing to severe and rapidly increasing leucocytosis, malignancy was highly suspected, but it was ruled out along with secondary hypereosinophilic syndrome after extensive investigations, and acute respiratory distress syndrome in this child was attributed to Idiopathic Hypereosinophilic Syndrome. Eosinophilia had a dramatic response to high dose corticosteroid therapy. To conclude, in patients with hypereosinophilic syndrome, possibility of progression to acute respiratory distress syndrome should be anticipated and managed accordingly.
儿童特发性高嗜酸性粒细胞综合征是一种罕见疾病。尽管对嗜酸性粒细胞疾病的认识有所提高,诊断方法也有了新进展,但由于病因因素的异质性,高嗜酸性粒细胞增多症的评估仍然具有挑战性。在急性临床环境中,由于这种情况不常遇到,管理计划往往不明确。它常与白细胞增多有关,但在无恶性肿瘤的情况下,导致多器官功能障碍的白细胞增多症很少见。一名此前健康的5岁男孩因发热、进行性咳嗽和呼吸困难2周就诊于我们的急诊室,病情迅速发展为呼吸衰竭和急性呼吸窘迫综合征。外周血涂片显示白细胞增多伴嗜酸性粒细胞增多,X线显示双侧肺部浸润及磨玻璃影,提示高嗜酸性粒细胞综合征伴继发性急性呼吸窘迫综合征。由于白细胞严重且迅速增加,高度怀疑为恶性肿瘤,但经过广泛检查后排除了恶性肿瘤及继发性高嗜酸性粒细胞综合征,该患儿的急性呼吸窘迫综合征归因于特发性高嗜酸性粒细胞综合征。嗜酸性粒细胞增多症对高剂量皮质类固醇治疗有显著反应。总之,对于高嗜酸性粒细胞综合征患者,应预期并相应处理进展为急性呼吸窘迫综合征的可能性。