Laboratory of Cell Biology, Neuroscience and Experimental Myology, Victor Babes National Institute of Pathology, 050096 Bucharest, Romania.
Department of Cell Biology and Histology, Carol Davila University of Medicine and Pharmacy, 050474 Bucharest, Romania.
Int J Mol Sci. 2022 Apr 27;23(9):4802. doi: 10.3390/ijms23094802.
Although they are considered rare disorders, muscular dystrophies have a strong impact on people's health. Increased disease severity with age, frequently accompanied by the loss of ability to walk in some people, and the lack of treatment, have directed the researchers towards the development of more effective therapeutic strategies aimed to improve the quality of life and life expectancy, slow down the progression, and delay the onset or convert a severe phenotype into a milder one. Improved understanding of the complex pathology of these diseases together with the tremendous advances in molecular biology technologies has led to personalized therapeutic procedures. Different approaches that are currently under extensive investigation require more efficient, sensitive, and less invasive methods. Due to its remarkable analytical sensitivity, droplet digital PCR has become a promising tool for accurate measurement of biomarkers that monitor disease progression and quantification of various therapeutic efficiency and can be considered a tool for non-invasive prenatal diagnosis and newborn screening. Here, we summarize the recent applications of droplet digital PCR in muscular dystrophy research and discuss the factors that should be considered to get the best performance with this technology.
虽然肌营养不良症被认为是罕见疾病,但它们对人们的健康有很大的影响。随着年龄的增长,疾病的严重程度增加,有些人经常会丧失行走能力,而且缺乏治疗方法,这促使研究人员开发出更有效的治疗策略,旨在提高生活质量和预期寿命,减缓疾病进展,延缓发病或使严重表型转变为较轻表型。对这些疾病复杂病理的深入了解以及分子生物学技术的巨大进步,促使了个性化治疗程序的出现。目前正在广泛研究的不同方法需要更有效、更敏感和更少侵入性的方法。由于其出色的分析灵敏度,液滴数字 PCR 已成为监测疾病进展和量化各种治疗效果的生物标志物的精确测量的有前途的工具,并且可以被认为是用于非侵入性产前诊断和新生儿筛查的工具。在这里,我们总结了液滴数字 PCR 在肌营养不良症研究中的最新应用,并讨论了使用该技术时应考虑的因素,以获得最佳性能。