Department of Dermatology, Cleveland Clinic Dermatology and Plastic Surgery Institute, 2049 E 100th St., Cleveland, OH, 44195, USA.
Department of Dermatology and Cutaneous Surgery, University of South Florida, Tampa, FL, USA.
Arch Dermatol Res. 2023 Oct;315(8):2413-2417. doi: 10.1007/s00403-022-02364-w. Epub 2022 Jul 18.
Although it is established that individuals with albinism have increased risks for nonmelanoma skin cancers, melanomas occurring in the setting of albinism are rare. PubMed and Google Scholar were searched for individual case reports describing melanoma in individuals with oculocutaneous albinism (OCA). All published cases characterizing individuals with albinism and melanoma in the medical literature were gathered to evaluate any epidemiologic or histologic differences from melanomas arising in the general population. Frequencies of melanoma characteristics between the OCA literature cohort and general population were compared using Clopper-Pearson confidence intervals. From 1952 to 2018, at least 64 cases of melanoma in 56 individuals with albinism were reported in the global medical literature. The median age of diagnosis for melanoma in individuals with albinism was 41 years, and the median Breslow depth at diagnosis was 2.0 mm. The subtypes of melanoma were nodular in 33% and superficial spreading in 46% of these cases, respectively. Amelanotic melanomas comprised 65% of the cases in our OCA cohort; however, histologic subtypes were only available for fourteen of the amelanotic cases. Finally, 17% of melanomas in patients with albinism arose from preexisting lesions. Despite their rarity, melanomas arising in oculocutaneous albinism have distinct characteristics from melanomas arising in the general population. Clinicians should consider a differential diagnosis of melanoma for any potential skin malignancies in individuals with albinism.
尽管已经确定白化病患者患非黑色素瘤皮肤癌的风险增加,但白化病患者中发生的黑色素瘤却很少见。在 PubMed 和 Google Scholar 上搜索了描述眼皮肤白化病(OCA)个体中黑色素瘤的个案报告。收集了医学文献中描述白化病个体和黑色素瘤的所有已发表病例,以评估其与普通人群中发生的黑色素瘤在流行病学或组织学上的任何差异。使用 Clopper-Pearson 置信区间比较 OCA 文献队列和普通人群中黑色素瘤特征的频率。从 1952 年到 2018 年,在全球医学文献中至少报道了 56 名白化病患者中的 64 例黑色素瘤病例。白化病患者黑色素瘤的中位诊断年龄为 41 岁,诊断时的中位 Breslow 深度为 2.0mm。这些病例中分别有 33%为结节性和 46%为浅表扩散型黑色素瘤。在我们的 OCA 队列中,无色素性黑色素瘤占 65%;然而,仅有 14 例无色素性病例的组织学亚型可供使用。最后,白化病患者的 17%的黑色素瘤源自先前存在的病变。尽管罕见,但眼皮肤白化病中发生的黑色素瘤与普通人群中发生的黑色素瘤具有明显不同的特征。临床医生应考虑对白化病患者的任何潜在皮肤恶性肿瘤进行黑色素瘤的鉴别诊断。