Department of Respiratory Medicine, Faculty of Medicine and Graduate School of Medicine, Hokkaido University, Japan.
Department of Diagnostic Imaging, Faculty of Medicine and Graduate School of Medicine, Hokkaido University, Japan.
Intern Med. 2023 Mar 1;62(5):763-767. doi: 10.2169/internalmedicine.0015-22. Epub 2022 Jul 22.
Pulmonary artery agenesis (PAA) is a rare congenital vascular anomaly usually diagnosed during infancy. We herein report a 67-year-old man with PAA manifesting as massive hemoptysis. Contrast-enhanced computed tomography of the chest revealed the diagnosis of PAA, which we speculated to have resulted in the present event. Detailed angiography provided more accurate information on the pulmonary vasculature and collateral circulation, which helped us plan tailored treatment. Although very rare, we must consider the possibility of PAA in adults with unexplained hemoptysis.
肺动脉发育不全(PAA)是一种罕见的先天性血管畸形,通常在婴儿期诊断。本文报告了一例 67 岁男性,因 PAA 表现为大咯血。胸部增强 CT 显示 PAA 的诊断,我们推测此次事件是由其引起。详细的血管造影提供了关于肺血管和侧支循环的更准确信息,这有助于我们制定针对性的治疗计划。尽管非常罕见,但我们必须考虑到不明原因咯血的成年人存在 PAA 的可能性。