Maron Barry J, Dearani Joseph A, Smedira Nicholas G, Schaff Hartzell V, Wang Shuiyun, Rastegar Hassan, Ralph-Edwards Anthony, Ferrazzi Paolo, Swistel Daniel, Shemin Richard J, Quintana Eduard, Bannon Paul G, Shekar Prem S, Desai Milind, Roberts William C, Lever Harry M, Adler Arnon, Rakowski Harry, Spirito Paolo, Nishimura Rick A, Ommen Steve R, Sherrid Mark V, Rowin Ethan J, Maron Martin S
Hypertrophic Cardiomyopathy Center, Lahey Hospital and Medical Center, Burlington, MA.
Mayo Clinic, Rochester, MN.
Am J Cardiol. 2022 Oct 1;180:124-139. doi: 10.1016/j.amjcard.2022.06.007. Epub 2022 Aug 12.
Surgical myectomy remains the time-honored primary treatment for hypertrophic cardiomyopathy patients with drug refractory limiting symptoms due to LV outflow obstruction. Based on >50 years experience, surgery reliably reverses disabling heart failure by permanently abolishing mechanical outflow impedance and mitral regurgitation, with normalization of LV pressures and preserved systolic function. A consortium of 10 international currently active myectomy centers report about 11,000 operations, increasing significantly in number over the most recent 15 years. Performed in experienced multidisciplinary institutions, perioperative mortality for myectomy has declined to 0.6%, becoming one of the safest currently performed open-heart procedures. Extended myectomy relieves symptoms in >90% of patients by ≥ 1 NYHA functional class, returning most to normal daily activity, and also with a long-term survival benefit; concomitant Cox-Maze procedure can reduce the number of atrial fibrillation episodes. Surgery, preferably performed in high volume clinical environments, continues to flourish as a guideline-based and preferred high benefit: low treatment risk option for adults and children with drug refractory disabling symptoms from obstruction, despite prior challenges: higher operative mortality/skepticism in 1960s/1970s; dual-chamber pacing in 1990s, alcohol ablation in 2000s, and now introduction of novel negative inotropic drugs potentially useful for symptom management.
对于因左心室流出道梗阻而出现药物难治性限制性症状的肥厚型心肌病患者,外科心肌切除术仍然是历史悠久的主要治疗方法。基于50多年的经验,手术通过永久消除机械性流出道阻力和二尖瓣反流,可靠地逆转致残性心力衰竭,使左心室压力恢复正常并保留收缩功能。一个由10个国际上目前仍在开展心肌切除术的中心组成的联盟报告了约11000例手术,在最近15年中数量显著增加。在经验丰富的多学科机构进行手术,心肌切除术的围手术期死亡率已降至0.6%,成为目前最安全的心脏直视手术之一。扩大性心肌切除术可使>90%的患者症状减轻≥1个纽约心脏协会(NYHA)心功能分级,使大多数患者恢复正常日常活动,并且还有长期生存益处;同期进行Cox迷宫手术可减少房颤发作次数。手术最好在高容量临床环境中进行,作为一种基于指南且高获益:低治疗风险的选择,对于因梗阻而出现药物难治性致残症状的成人和儿童患者,手术仍在蓬勃发展,尽管此前面临诸多挑战:20世纪60年代/70年代手术死亡率较高/受到质疑;20世纪90年代的双腔起搏、21世纪初的酒精消融,以及现在引入可能对症状管理有用的新型负性肌力药物。