Sim Young Woo, Kim Young Seon, Lee Seung Eun, Jang Min Hye
Taehan Yongsang Uihakhoe Chi. 2022 May;83(3):744-749. doi: 10.3348/jksr.2021.0103. Epub 2021 Dec 11.
Fibrosing mediastinitis is a rare benign disorder characterized by the proliferation of dense fibrous tissue within the mediastinum. It typically manifests as localized or infiltrative soft-tissue masses in the middle mediastinum or hilar area, which cause compression and encasement of adjacent mediastinal structures, such as the vessels or airway. Here, we report a rare case of fibrosing mediastinitis in a 13-year-old girl that presented as a middle mediastinal mass lesion on CT scan with obliterating left lower lobar bronchus. The patient's symptoms and follow-up chest CT showed significant improvement following systemic corticosteroid treatment. As fibrosing mediastinitis can improve with systemic steroid therapy, radiologists must be aware of its radiologic findings when discriminating between infiltrating soft tissue lesions in the mediastinum.
纤维性纵隔炎是一种罕见的良性疾病,其特征是纵隔内致密纤维组织增生。它通常表现为中纵隔或肺门区域的局限性或浸润性软组织肿块,可导致相邻纵隔结构如血管或气道受压和包绕。在此,我们报告一例13岁女孩的罕见纤维性纵隔炎病例,CT扫描显示为中纵隔肿块病变,左下叶支气管闭塞。全身使用皮质类固醇治疗后,患者的症状及后续胸部CT显示有显著改善。由于纤维性纵隔炎可通过全身类固醇治疗得到改善,放射科医生在鉴别纵隔浸润性软组织病变时必须了解其影像学表现。