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一名77岁男性的法洛四联症伴发绀。

Cyanotic tetralogy of Fallot in a 77 year old man.

作者信息

Thomas S H, Bass P, Pambakian H, Marigold J H

机构信息

Department of Medicine for the Elderly, St Thomas' Hospital, London, UK.

出版信息

Postgrad Med J. 1987 May;63(739):361-2. doi: 10.1136/pgmj.63.739.361.

DOI:10.1136/pgmj.63.739.361
PMID:3671268
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC2428473/
Abstract

We report the clinical details of a 77 year old man with classical tetralogy of Fallot. The patient had clubbing and cyanosis at birth, and exertional squatting in childhood. He was asymptomatic as an adult until the seventh decade, when he developed biventricular failure and had an episode of bacterial endocarditis. He finally died of cerebral infarction and bronchopneumonia following abdominal surgery. In spite of investigations, the diagnosis was not made in life, but only discovered at post-mortem. A persistent ductus arteriosus was also found. Increased pulmonary blood flow via the ductus is believed to have facilitated this patient's unusual longevity.

摘要

我们报告了一名患有典型法洛四联症的77岁男性的临床细节。该患者出生时即有杵状指和发绀,童年时出现劳力性蹲踞。成年后直至七十多岁一直无症状,之后出现双心室衰竭并发生了一次细菌性心内膜炎。他最终在腹部手术后死于脑梗死和支气管肺炎。尽管进行了检查,但生前未作出诊断,仅在尸检时发现。还发现了持续性动脉导管未闭。据信通过动脉导管增加的肺血流量促进了该患者不同寻常的长寿。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b9f/2428473/da09298522f9/postmedj00197-0040-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b9f/2428473/da09298522f9/postmedj00197-0040-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2b9f/2428473/da09298522f9/postmedj00197-0040-a.jpg

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1
Cyanotic tetralogy of Fallot in a 77 year old man.一名77岁男性的法洛四联症伴发绀。
Postgrad Med J. 1987 May;63(739):361-2. doi: 10.1136/pgmj.63.739.361.
2
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引用本文的文献

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'Superimposed miracles': an extremely rare case of a septuagenarian with an unrepaired tetralogy of Fallot: a case report.“叠加的奇迹”:一名患有未修复法洛四联症的七旬老人的极其罕见病例:病例报告
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2
An Adult Patient With a Tetralogy of Fallot Case.一名法洛四联症成年患者病例。
Cureus. 2020 Nov 23;12(11):e11658. doi: 10.7759/cureus.11658.
3
Challenges Faced in Managing an Adult Uncorrected Tetralogy of Fallot Patient with Pneumonia and Septic Shock in the Intensive Care Unit.

本文引用的文献

1
TETRALOGY OF FALLOT ASSOCIATED WITH WELL DEVELOPED LEFT VENTRICULAR MUSCLE MASS AND INCREASED LIFE SPAN.法洛四联症合并左心室肌肉质量发育良好及寿命延长
Am J Med. 1964 Jan;36:54-61. doi: 10.1016/0002-9343(64)90147-0.
2
Tetralogy of Fallot in adults. A report on 147 patients.成人法洛四联症。147例患者的报告。
Am J Med. 1979 May;66(5):811-6. doi: 10.1016/0002-9343(79)91121-5.
在重症监护病房管理一名患有肺炎和感染性休克的未矫正法洛四联症成年患者时面临的挑战。
Indian J Crit Care Med. 2020 Nov;24(11):1135-1136. doi: 10.5005/jp-journals-10071-23648.
4
Clinical and postmortem findings of pentalogy of Fallot in an 18-month-old Holstein heifer.一头18月龄荷斯坦小母牛法洛四联症的临床及尸检结果。
J Vet Med Sci. 2019 Dec 5;81(11):1676-1679. doi: 10.1292/jvms.19-0147. Epub 2019 Oct 1.
5
A Long-Term Survivor with Tetralogy of Fallot Treated Only with the Classical Blalock-Taussig Shunt.一名仅接受经典布莱洛克-陶西格分流术治疗的法洛四联症长期存活者。
Case Rep Cardiol. 2018 Aug 19;2018:5262745. doi: 10.1155/2018/5262745. eCollection 2018.
6
Anaesthetic management for drainage of frontoparietal abscess in a patient of uncorrected Tetralogy of Fallot.法洛四联症未矫治患者额顶叶脓肿引流的麻醉管理
Indian J Anaesth. 2015 Apr;59(4):244-6. doi: 10.4103/0019-5049.155003.
7
[First diagnosis of Fallot tetralogy in a 74-year-old man].[一名74岁男性首次诊断为法洛四联症]
Z Kardiol. 2005 Mar;94(3):205-10. doi: 10.1007/s00392-005-0203-8.