Thomas S H, Bass P, Pambakian H, Marigold J H
Department of Medicine for the Elderly, St Thomas' Hospital, London, UK.
Postgrad Med J. 1987 May;63(739):361-2. doi: 10.1136/pgmj.63.739.361.
We report the clinical details of a 77 year old man with classical tetralogy of Fallot. The patient had clubbing and cyanosis at birth, and exertional squatting in childhood. He was asymptomatic as an adult until the seventh decade, when he developed biventricular failure and had an episode of bacterial endocarditis. He finally died of cerebral infarction and bronchopneumonia following abdominal surgery. In spite of investigations, the diagnosis was not made in life, but only discovered at post-mortem. A persistent ductus arteriosus was also found. Increased pulmonary blood flow via the ductus is believed to have facilitated this patient's unusual longevity.
我们报告了一名患有典型法洛四联症的77岁男性的临床细节。该患者出生时即有杵状指和发绀,童年时出现劳力性蹲踞。成年后直至七十多岁一直无症状,之后出现双心室衰竭并发生了一次细菌性心内膜炎。他最终在腹部手术后死于脑梗死和支气管肺炎。尽管进行了检查,但生前未作出诊断,仅在尸检时发现。还发现了持续性动脉导管未闭。据信通过动脉导管增加的肺血流量促进了该患者不同寻常的长寿。