Kabra Ruchita, Kumar Sunil, Acharya Sourya, Bhansali Pratik J, Daiya Varun
Department of Medicine, Jawaharlal Nehru Medical College, Datta Meghe Institute of Medical Sciences (Deemed to be University), Wardha, IND.
Department of Radiodiagnosis, Jawaharlal Nehru Medical College, Datta Meghe Institute of Medical Sciences (Deemed to be University), Wardha, IND.
Cureus. 2023 Feb 13;15(2):e34916. doi: 10.7759/cureus.34916. eCollection 2023 Feb.
Acute respiratory distress syndrome (ARDS)-like symptoms and rapid progression characterize the interstitial lung disease known as acute interstitial pneumonitis, also known as Hamman-Rich syndrome. It has a bad prognosis and a high incidence of mortality. We describe the case of a 25-year-old male patient with acute-onset type I respiratory failure with detrimental X-ray abnormalities who presented to the emergency room without any history of pulmonary disease or smoking. The provisional diagnosis of Hamman-Rich syndrome was reached after other clinical entities were ruled out based on CT findings. Myocardial hypokinesis of the apex and septum, as well as a modest systolic dysfunction (ejection fraction: 50%) similar to acute myocarditis, were detected by echocardiogram. Acute myocarditis in the setting of Hamman-Rich syndrome has been anecdotally reported and its mechanism remains to be elucidated.
急性间质性肺炎(又称Hamman-Rich综合征)是一种间质性肺病,具有类似急性呼吸窘迫综合征(ARDS)的症状且病情进展迅速。其预后不良,死亡率高。我们描述了一名25岁男性患者的病例,该患者急性起病,出现I型呼吸衰竭,胸部X线检查有不良异常表现,就诊于急诊室时无任何肺部疾病或吸烟史。根据CT检查结果排除其他临床疾病后,初步诊断为Hamman-Rich综合征。超声心动图检查发现心尖和室间隔心肌运动减弱,以及类似于急性心肌炎的轻度收缩功能障碍(射血分数:50%)。Hamman-Rich综合征合并急性心肌炎已有个案报道,但其机制仍有待阐明。