Kuriakose Jyothsna, Sundararaj Jenifer Jeba, Joseph Jewell, Gladys Anitha, Kurien Richu Bob, Manoharan Aishwarya, As Chandhu
Palliative Medicine, Christian Medical College and Hospital Vellore, Vellore, Tamil Nadu, India.
Palliative Medicine, Christian Medical College and Hospital Vellore, Vellore, Tamil Nadu, India
BMJ Support Palliat Care. 2024 Dec 19;14(e3):e2534-e2536. doi: 10.1136/spcare-2023-004588.
Occupational exposure to silica has been seldom implicated to cause systemic sclerosis. Erasmus syndrome is a rare condition where there is development of systemic sclerosis following silicosis. Early diagnosis is essential for appropriate treatment and symptom control. We describe a 42-year-old stone cutter with silicosis who was subsequently diagnosed to have diffuse pattern of systemic sclerosis. A multidisciplinary team including pulmonologists, specialist palliative care physicians, rheumatologists and radiologists were involved in diagnosis and management. Timely diagnosis and a multidisciplinary team management with pharmacological and non-pharmacological measures was essential in holistic care provision. This is the first report of specialist palliative care team facilitating diagnosis of this rare syndrome and promoting integration in the overall care and management.
职业性接触二氧化硅很少被认为会导致系统性硬化症。伊拉斯谟综合征是一种罕见的病症,在矽肺后会出现系统性硬化症。早期诊断对于适当治疗和症状控制至关重要。我们描述了一名42岁患有矽肺的石匠,随后被诊断为弥漫型系统性硬化症。一个包括肺科医生、专科姑息治疗医生、风湿病学家和放射科医生的多学科团队参与了诊断和管理。及时诊断以及采用药物和非药物措施的多学科团队管理对于提供全面护理至关重要。这是关于专科姑息治疗团队协助诊断这种罕见综合征并促进其融入整体护理和管理的首份报告。