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一例巨大睾丸旁黏液样脂肪肉瘤病例报告。

A case report of giant paratesticular myxoid liposarcoma.

作者信息

Fouimtizi Jaafar, Maachi Youssef, Rhayour Anass, El Boustani Amine, Slaoui Amine, Karmouni Tariq, El Khader Khalid, Koutani Abdellatif, Iben Attya Andaloussi Ahmed

机构信息

Urology B Department, Avicenne Hospital, University Hospital Center IBN SINA, University Mohammed V, Rabat, Morocco.

出版信息

Urol Case Rep. 2024 Apr 29;54:102747. doi: 10.1016/j.eucr.2024.102747. eCollection 2024 May.

DOI:10.1016/j.eucr.2024.102747
PMID:38711673
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11070593/
Abstract

Liposarcomas are an uncommon occurrence in the paratesticular region that makes about 20 % of all sarcomas. The clinical appearance is an inguinal lump, which can resemble a hydrocele or hernia. There would be no conventional treatment accessible because it is such a rare disease. We report the case of a 68-year-old man with paratesticular myxoid liposarcoma. Ultrasound and CT-scan came back in favor of a paratesticular tumor. A high inguinal orchidectomy has been done and the diagnostic of myxoid liposarcoma was first evoked by histology and confirmed by molecular biology. At 12 months follow up the patient remains tumor free.

摘要

脂肪肉瘤在睾丸旁区域并不常见,约占所有肉瘤的20%。临床表现为腹股沟肿块,可能类似鞘膜积液或疝气。由于这种疾病非常罕见,没有常规的治疗方法。我们报告一例68岁患有睾丸旁黏液样脂肪肉瘤的男性病例。超声和CT扫描结果支持睾丸旁肿瘤的诊断。已进行高位腹股沟睾丸切除术,组织学检查首先怀疑为黏液样脂肪肉瘤,分子生物学检查予以证实。随访12个月,患者无肿瘤复发。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/90dd/11070593/4256237029cf/gr5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/90dd/11070593/aa52f8d8bbd6/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/90dd/11070593/87e4b9a62ba4/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/90dd/11070593/9042b76fa044/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/90dd/11070593/49d5c748b1d9/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/90dd/11070593/4256237029cf/gr5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/90dd/11070593/aa52f8d8bbd6/gr1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/90dd/11070593/87e4b9a62ba4/gr2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/90dd/11070593/9042b76fa044/gr3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/90dd/11070593/49d5c748b1d9/gr4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/90dd/11070593/4256237029cf/gr5.jpg

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本文引用的文献

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An MRI-based decision tree to distinguish lipomas and lipoma variants from well-differentiated liposarcoma of the extremity and superficial trunk: Classification and regression tree (CART) analysis.基于 MRI 的决策树鉴别肢体和浅表躯干的良、恶性脂肪肉瘤及脂肪肉瘤变异型:分类回归树(CART)分析。
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About a case of paratesticular myxoid liposarcoma.关于一例睾丸旁黏液样脂肪肉瘤。
Urol Case Rep. 2018 Aug 22;21:27-28. doi: 10.1016/j.eucr.2018.08.011. eCollection 2018 Nov.
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Giant paratesticular liposarcoma: A case report and review of the literature.巨大睾丸旁脂肪肉瘤:一例报告并文献复习
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Current management of liposarcoma of the spermatic cord: A case report and review of the literature.精索脂肪肉瘤的当前管理:一例病例报告及文献综述。
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Prognostic factors and outcome of spermatic cord sarcoma.精索肉瘤的预后因素及结局
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Descriptive epidemiology of sarcomas in Europe: report from the RARECARE project.欧洲肉瘤的描述性流行病学:来自 RARECARE 项目的报告。
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