Center for Lymphatic Disorders, Children's Hospital of Philadelphia, University of Pennsylvania.
Center for Lymphatic Disorders, Children's Hospital of Philadelphia, University of Pennsylvania.
Semin Pediatr Surg. 2024 Jun;33(3):151420. doi: 10.1016/j.sempedsurg.2024.151420. Epub 2024 May 23.
Patients with central lymphatic conduction disorders commonly have recalcitrant pleural effusions and or ascites. These conditions cause a profound deterioration in the patient's quality of life. Support measures such as low-fat diet and diuretics alone hardly ever provide meaningful improvement. New understanding of the pathophysiology of these disorders has opened the door in recent years to the development of several surgical procedures that have remarkable success rates. However, these patients must be managed by expert multidisciplinary teams.
患有中枢淋巴传导障碍的患者常伴有顽固的胸腔积液和/或腹水。这些病症会严重降低患者的生活质量。单纯采用低脂饮食和利尿剂等支持措施几乎无法带来明显改善。近年来,对这些病症病理生理学的新认识为开发几种成功率显著的手术方法开辟了道路。然而,这些患者必须由专家多学科团队进行管理。